faktor XII [Factor XII]

tematický
18
Termíny

glass faktor
Hagemanův faktor
koagulační faktor XII

 

Coagulation Factor XII
Factor 12
Factor Twelve
Hageman Factor

Perzistentní odkaz   https://www.medvik.cz/link/D005174
Definice

Stabilní krevní koagulační faktor aktivovaný kontaktem se subendoteliálním povrchem poraněné cévy. Spolu s prekalikreinem slouží jako kontaktní faktor, který iniciuje vnitřní cestu koagulace krve. Kalikrein aktivuje faktor XII až XIIa. Nedostatek faktoru XII, nazývaný také Hagemanova choroba, vede ke zvýšenému výskytu tromboembolické nemoci. Mutace v genu pro faktor XII, které zřejmě zvyšují amidolytickou aktivitu faktoru XII, jsou spojeny s hereditárním angioedémem typu III.

Stable blood coagulation factor activated by contact with the subendothelial surface of an injured vessel. Along with prekallikrein, it serves as the contact factor that initiates the intrinsic pathway of blood coagulation. Kallikrein activates factor XII to XIIa. Deficiency of factor XII, also called the Hageman trait, leads to increased incidence of thromboembolic disease. Mutations in the gene for factor XII that appear to increase factor XII amidolytic activity are associated with HEREDITARY ANGIOEDEMA TYPE III.

DUI
D005174 MeSH Prohlížeč
CUI
M0008158
CAS
Blood-coagulation factor XII
Historická pozn.
66(64)
Veřejná pozn.
66

D Chemikálie a léčiva
D08.622.184 chymotrypsinogen 5
D08.622.355 faktor IX 82
D08.622.432 faktor VII 55
D08.622.471 faktor X 36
D08.622.490 faktor XI 4
D08.622.500 faktor XII 18
D08.622.505 faktor XIII 14
D08.622.509 pepsinogeny 16
D08.622.610 plazminogen 43
D08.622.658 prekalikrein 6
D08.622.705 protein C 111
D08.622.709 protrombin 115
D08.622.885 trypsinogen 22
D12.776 proteiny 2 575
D12.776.124 krevní proteiny 909
D12.776.124.125 koagulační faktory 332
D12.776.124.125.050 beta-thromboglobulin 7
D12.776.124.125.300 faktor V 93
D12.776.124.125.325 faktor VII 55
D12.776.124.125.350 faktor VIII 310
D12.776.124.125.375 faktor IX 82
D12.776.124.125.400 faktor X 36
D12.776.124.125.425 faktor XI 4
D12.776.124.125.450 faktor XII 18
D12.776.124.125.450.324 faktor XIIa 2
D12.776.124.125.475 faktor XIII 14
D12.776.124.125.500 fibrinogen 483
D12.776.124.125.515 fibrinopeptid A 9
D12.776.124.125.530 fibrinopeptid B 6
D12.776.124.125.597 kalikreiny 39
D12.776.124.125.635 kininogeny 7
D12.776.124.125.662 aktivátory plazminogenu 56
D12.776.124.125.691 trombocytový faktor 3 4
D12.776.124.125.720 trombocytový faktor 4 18
D12.776.124.125.800 protrombin 115
D12.776.124.125.890 trombin 228
D12.776.124.125.900 tkáňový faktor 57
D12.776.124.125.920 von Willebrandův faktor 131
D12.776.811 proteinové prekurzory 131
D12.776.811.243 prekurzory enzymů 68
D12.776.811.243.184 chymotrypsinogen 5
D12.776.811.243.200 komplement - faktor B 3
D12.776.811.243.355 faktor IX 82
D12.776.811.243.432 faktor VII 55
D12.776.811.243.471 faktor X 36
D12.776.811.243.490 faktor XI 4
D12.776.811.243.500 faktor XII 18
D12.776.811.243.505 faktor XIII 14
D12.776.811.243.509 pepsinogeny 16
D12.776.811.243.610 plazminogen 43
D12.776.811.243.658 prekalikrein 6
D12.776.811.243.705 protein C 111
D12.776.811.243.709 protrombin 115
D12.776.811.243.885 trypsinogen 22
D23.119.100 vápník 2 823
D23.119.300 faktor V 93
D23.119.325 faktor VII 55
D23.119.350 faktor VIII 310
D23.119.375 faktor IX 82
D23.119.400 faktor X 36
D23.119.425 faktor XI 4
D23.119.450 faktor XII 18
D23.119.450.324 faktor XIIa 2
D23.119.475 faktor XIII 14
D23.119.490 fibrinogen 483
D23.119.500 fibrinopeptid A 9
D23.119.510 fibrinopeptid B 6
D23.119.597 kalikreiny 39
D23.119.630 kininogeny 7
D23.119.945 protrombin 115
D23.119.960 trombin 228
D23.119.965 tkáňový faktor 57

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