faktor IX [Factor IX]

tematický
82
Termíny

antihemofilický faktor B
autoprothrombin II
Christmasův faktor
koagulační faktor IX
plazmatická tromboplastická komponenta

 

Autoprothrombin II
Blood Coagulation Factor IX
Christmas Factor
Coagulation Factor IX
Factor 9
Factor IX Complex
Factor IX Fraction
Factor Nine
Plasma Thromboplastin Component

Perzistentní odkaz   https://www.medvik.cz/link/D005164
Definice

Faktor krevní srážlivosti, který je stabilní při skladování a působí ve vnitřní dráze krevní koagulace. Jeho aktivovaná forma, IXa, tvoří komplex s faktorem VIII a vápníkem na destičkovém faktoru 3 a aktivuje faktor X na Xa. Nedostatek faktoru IX má za následek hemofilii B (Christmasovu chorobu).

Storage-stable blood coagulation factor acting in the intrinsic pathway of blood coagulation. Its activated form, IXa, forms a complex with factor VIII and calcium on platelet factor 3 to activate factor X to Xa. Deficiency of factor IX results in HEMOPHILIA B (Christmas Disease).

DUI
D005164 MeSH Prohlížeč
CUI
M0008141
RN
9001-28-9
CAS
Blood-coagulation factor IX

D Chemikálie a léčiva
D08.622.184 chymotrypsinogen 5
D08.622.355 faktor IX 82
D08.622.432 faktor VII 55
D08.622.471 faktor X 36
D08.622.490 faktor XI 4
D08.622.500 faktor XII 18
D08.622.505 faktor XIII 14
D08.622.509 pepsinogeny 16
D08.622.610 plazminogen 43
D08.622.658 prekalikrein 6
D08.622.705 protein C 111
D08.622.709 protrombin 115
D08.622.885 trypsinogen 22
D12.776 proteiny 2 575
D12.776.124 krevní proteiny 909
D12.776.124.125 koagulační faktory 332
D12.776.124.125.050 beta-thromboglobulin 7
D12.776.124.125.300 faktor V 93
D12.776.124.125.325 faktor VII 55
D12.776.124.125.350 faktor VIII 309
D12.776.124.125.375 faktor IX 82
D12.776.124.125.375.310 faktor IXa 6
D12.776.124.125.400 faktor X 36
D12.776.124.125.425 faktor XI 4
D12.776.124.125.450 faktor XII 18
D12.776.124.125.475 faktor XIII 14
D12.776.124.125.500 fibrinogen 483
D12.776.124.125.515 fibrinopeptid A 9
D12.776.124.125.530 fibrinopeptid B 6
D12.776.124.125.597 kalikreiny 39
D12.776.124.125.635 kininogeny 7
D12.776.124.125.662 aktivátory plazminogenu 56
D12.776.124.125.691 trombocytový faktor 3 4
D12.776.124.125.720 trombocytový faktor 4 18
D12.776.124.125.800 protrombin 115
D12.776.124.125.890 thrombin 227
D12.776.124.125.900 tkáňový faktor 57
D12.776.124.125.920 von Willebrandův faktor 131
D12.776.811 proteinové prekurzory 131
D12.776.811.243 prekurzory enzymů 68
D12.776.811.243.184 chymotrypsinogen 5
D12.776.811.243.200 komplement - faktor B 3
D12.776.811.243.355 faktor IX 82
D12.776.811.243.432 faktor VII 55
D12.776.811.243.471 faktor X 36
D12.776.811.243.490 faktor XI 4
D12.776.811.243.500 faktor XII 18
D12.776.811.243.505 faktor XIII 14
D12.776.811.243.509 pepsinogeny 16
D12.776.811.243.610 plazminogen 43
D12.776.811.243.658 prekalikrein 6
D12.776.811.243.705 protein C 111
D12.776.811.243.709 protrombin 115
D12.776.811.243.885 trypsinogen 22
D23.119.100 vápník 2 819
D23.119.300 faktor V 93
D23.119.325 faktor VII 55
D23.119.350 faktor VIII 309
D23.119.375 faktor IX 82
D23.119.375.310 faktor IXa 6
D23.119.400 faktor X 36
D23.119.425 faktor XI 4
D23.119.450 faktor XII 18
D23.119.475 faktor XIII 14
D23.119.490 fibrinogen 483
D23.119.500 fibrinopeptid A 9
D23.119.510 fibrinopeptid B 6
D23.119.597 kalikreiny 39
D23.119.630 kininogeny 7
D23.119.945 protrombin 115
D23.119.960 thrombin 227
D23.119.965 tkáňový faktor 57

Užší termíny