46, XX Disorders of Sex Development [poruchy sexuálního vývoje s karyotypem 46, XX]

topical
20
Terms

ženský pseudohermafroditismus

 

46, XX DSD
46,XX Disorders of Sex Development
46,XX DSD
Female Pseudohermaphroditism

Persistent link   https://www.medvik.cz/link/D058489
Definition

Congenital conditions in individuals with a female karyotype, in which the development of the gonadal or anatomical sex is atypical.

DUI
D058489 MeSH Browser
CUI
M0542824
History note
2011; for FEMALE PSEUDOHERMAPHRODITISM use DISORDERS OF SEX DEVELOPMENT 2006-2010
Public note
2011; for FEMALE PSEUDOHERMAPHRODITISM see PSEUDOHERMAPHRODITISM 2006-2010

C Diseases
C12.050.351.875 Urogenital Abnormalities 145
C12.050.351.875.253 Disorders of Sex Development 231
C12.050.351.875.253.064 46, XX Disorders of Sex Development 20
C12.050.351.875.253.064.249 Gonadal Dysgenesis, 46,XX 2
C12.050.351.875.253.064.500 Hyperandrogenism 107
C12.050.351.875.253.090 Adrenogenital Syndrome 50
C12.050.351.875.253.096 Disorder of Sex Development, 46,XY 8
C12.050.351.875.253.309 Gonadal Dysgenesis 59
C12.200.706.316 Disorders of Sex Development 231
C12.200.706.316.064.249 Gonadal Dysgenesis, 46,XX 2
C12.200.706.316.064.500 Hyperandrogenism 107
C12.200.706.316.090 Adrenogenital Syndrome 50
C12.200.706.316.309 Gonadal Dysgenesis 59
C12.800.316.064.249 Gonadal Dysgenesis, 46,XX 2
C12.800.316.064.500 Hyperandrogenism 107
C12.800.316.090 Adrenogenital Syndrome 50
C12.800.316.309 Gonadal Dysgenesis 59
C16.131.939.316 Disorders of Sex Development 231
C16.131.939.316.064.249 Gonadal Dysgenesis, 46,XX 2
C16.131.939.316.064.500 Hyperandrogenism 107
C16.131.939.316.129 Adrenogenital Syndrome 50
C16.131.939.316.309 Gonadal Dysgenesis 59
C19.391.119.064.249 Gonadal Dysgenesis, 46,XX 2
C19.391.119.064.500 Hyperandrogenism 107
C19.391.119.090 Adrenogenital Syndrome 50
C19.391.119.309 Gonadal Dysgenesis 59