Atypical Hemolytic Uremic Syndrome [atypický hemolyticko-uremický syndrom]

topical
41
Terms

neenteropatický HUS

 

Atypical Hemolytic-Uremic Syndrome
Hemolytic Uremic Syndrome, Atypical
Non-Shiga-Like Toxin-Associated HUS
Non-Stx-Hus
Nonenteropathic HUS

Persistent link   https://www.medvik.cz/link/D065766
Definition

An hereditary hemolytic uremic syndrome associated with variations in the gene that encodes COMPLEMENT FACTOR H, or the related proteins CFHR1 and CFHR3. Disease often progresses to CHRONIC KIDNEY FAILURE without the prodromal symptoms of ENTEROCOLITIS and DIARRHEA that characterize typical hemolytic uremic syndrome.

DUI
D065766 MeSH Browser
CUI
M0532727
History note
2015; use Hemolytic-Uremic Syndrome 2010-2014
Public note
2015; see HEMOLYTIC-UREMIC SYNDROME 2010-2014;

C Diseases
C12.050.351.968 Urologic Diseases 834
C12.050.351.968.419 Kidney Diseases 3 059
C12.050.351.968.419.936 Uremia 227
C12.050.351.968.419.936.463 Hemolytic-Uremic Syndrome 180
C12.050.351.968.419.936.463.500 Atypical Hemolytic Uremic Syndrome 41
C12.200.777 Urologic Diseases 834
C12.200.777.419 Kidney Diseases 3 059
C12.200.777.419.936 Uremia 227
C12.200.777.419.936.463 Hemolytic-Uremic Syndrome 180
C12.200.777.419.936.463.500 Atypical Hemolytic Uremic Syndrome 41
C12.950.419 Kidney Diseases 3 059
C12.950.419.936 Uremia 227
C12.950.419.936.463 Hemolytic-Uremic Syndrome 180
C12.950.419.936.463.500 Atypical Hemolytic Uremic Syndrome 41
C15.378.050 Anemia 1 244
C15.378.050.141 Anemia, Hemolytic 257
C15.378.050.141.610 Hemolytic-Uremic Syndrome 180
C15.378.050.141.610.500 Atypical Hemolytic Uremic Syndrome 41
C15.378.140.855 Thrombocytopenia 601
C15.378.140.855.925 Thrombotic Microangiopathies 62
C15.378.140.855.925.500 Hemolytic-Uremic Syndrome 180
C15.378.140.855.925.500.500 Atypical Hemolytic Uremic Syndrome 41
C15.378.243 Cytopenia 2
C15.378.243.937 Thrombocytopenia 601
C15.378.243.937.925 Thrombotic Microangiopathies 62
C15.378.243.937.925.500 Hemolytic-Uremic Syndrome 180
C15.378.243.937.925.500.500 Atypical Hemolytic Uremic Syndrome 41