Polandův syndrom (PS) je vzácná vrozená anomálie doprovázená jednostrannou absencí musculus pectoralis maior s ipsilaterální deformitou hrudní stěny a horní končetiny. Kombinace PS a dextrokardie je velmi neobvyklá, dodnes bylo publikováno pouze 20 případů. Pokud je koexistence dextrokardie u PS přítomna, je téměř vždy spojena s levostrannými deformitami hrudníku. Prezentujeme devítiměsíčního kojence s levostranným PS v kombinaci s izolovanou dextrokardií a částečnou agenezí 3. a 4. žebra vlevo.

Poland syndrome (PS) is a rare congenital anomaly accompanied by the unilateral absence of the pectoralis major, and the ipsilateral chest-wall and upper-limb deformity. The combination of PS and dextrocardia is very uncommon, only 20 cases having been published until now. If coexistence of dextrocardia in PS is present, it is almost always associated with left chest deformities. We present a nine-month-old infant with left-sided PS associated with isolated dextrocardia and partial agenesis of the 3rd and 4th left ribs.

• MeSH
• Dextrocardia * diagnostic imaging   diagnosis   etiology   MeSH
• Thoracic Wall abnormalities   MeSH
• Infant MeSH
• Humans MeSH
• Poland Syndrome * diagnostic imaging   diagnosis   epidemiology   MeSH
• Pectoralis Muscles abnormalities   MeSH
• Ribs abnormalities   MeSH
• Check Tag
• Infant MeSH
• Humans MeSH
• Female MeSH
• Publication type
• Case Reports MeSH
• Research Support, Non-U.S. Gov't MeSH