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A unique case of embolic myocardial infarction in a 22-year-old woman with Fontan circulation
Marianna Vachalcová, Marta Jakubová, Martin Czerny, Alžbeta Bánovčinová, Silvia Mišíková, Allan Böhm, Karolina Angela Sieradzka, Pavol Török, Gabriel Valočik, Ingrid Schusterová
Language English Country Czech Republic
Document type Case Reports
- MeSH
- Anticoagulants therapeutic use MeSH
- Fontan Procedure MeSH
- Myocardial Infarction * diagnosis etiology therapy MeSH
- Humans MeSH
- Young Adult MeSH
- Postoperative Complications MeSH
- Thromboembolism MeSH
- Treatment Outcome MeSH
- Check Tag
- Humans MeSH
- Young Adult MeSH
- Female MeSH
- Publication type
- Case Reports MeSH
Embólia koronárnych artérií je menej častou príčinou akútneho infarktu myokardu. Predstavujeme kazuistiku 22-ročnej pacientky s dvojvtokovou ľavou komorou, defektom komorového septa a pulmonálnou stenózou po Fontanovej operácii s akútnym spodným STEMI na embolickom podklade. Okrem známych rizík vedúcich k trombotickým komplikáciám spojeným s Fontanovskou cirkuláciou, medzi potenciálne predisponujúce faktory trombembolizmu u tejto pacientky patrili vytvorenie trombu v dolnej dutej žile a nedostatočná antikoagulačná liečba. Táto kazuistika predstavuje jednu z prvých dokumentovaných embolických príčin STEMI u pacienta s Fontanovskou cirkuláciou. Doteraz nie je vytvorený konsenzus, že antikoagulačná terapia warfarínom je u pacientov s Fontanovskou cirkuláciou superiórna voči aspirínu v primárnej prevencii trombembolických príhod.
Coronary artery embolism is an uncommon cause of acute myocardial infarction. We present a case of a 22-year-old patient with double inlet left ventricle (DILV), ventricular septal defect and pulmonary stenosis after Fontan repair with an acute embolic inferior ST-segment elevation myocardial infarction (STEMI). Apart from already known risk factors of thrombotic complications associated with Fontan circulation, additional predispositions in this patient included thrombus formation located in the inferior vena cava and the lack of anticoagulation therapy. This is one of the first reported embolic causes of STEMI in a patient with a Fontan circulation. Up to date, there is no consensus that anticoagulation therapy with warfarin is superior to aspirin in primary prevention of thromboembolism in patients with Fontan circulation.
Clinic of Anesthesiology East Slovak Institute of Cardiovascular Diseases Košice
Department of Arrhythmias East Slovak Insititute of Cardiovascular Diseases Košice
Department of Cardiology East Slovak Institute of Cardiovascular Diseases Košice
Department of Cardiovascular Surgery University Heart Center Freiburg Bad Krozingen Freiburg Germany
Department of Functional Diagnostics East Slovak Institute of Cardiovascular Diseases Košice
References provided by Crossref.org
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- $a Embólia koronárnych artérií je menej častou príčinou akútneho infarktu myokardu. Predstavujeme kazuistiku 22-ročnej pacientky s dvojvtokovou ľavou komorou, defektom komorového septa a pulmonálnou stenózou po Fontanovej operácii s akútnym spodným STEMI na embolickom podklade. Okrem známych rizík vedúcich k trombotickým komplikáciám spojeným s Fontanovskou cirkuláciou, medzi potenciálne predisponujúce faktory trombembolizmu u tejto pacientky patrili vytvorenie trombu v dolnej dutej žile a nedostatočná antikoagulačná liečba. Táto kazuistika predstavuje jednu z prvých dokumentovaných embolických príčin STEMI u pacienta s Fontanovskou cirkuláciou. Doteraz nie je vytvorený konsenzus, že antikoagulačná terapia warfarínom je u pacientov s Fontanovskou cirkuláciou superiórna voči aspirínu v primárnej prevencii trombembolických príhod.
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