Moyamoya disease associated with fibromuscular dysplasia of intrapulmonary bronchial arteries-a case report
Language English Country United States Media print-electronic
Document type Case Reports, Journal Article
PubMed
31869771
DOI
10.1016/j.carpath.2019.107182
PII: S1054-8807(19)30347-3
Knihovny.cz E-resources
- Keywords
- Bronchial artery, Fibromuscular dysplasia, Moyamoya disease,
- MeSH
- Bronchial Arteries pathology MeSH
- Carotid Arteries diagnostic imaging pathology surgery MeSH
- Cerebral Arteries diagnostic imaging pathology surgery MeSH
- Biopsy MeSH
- Angiography, Digital Subtraction MeSH
- Adult MeSH
- Fatal Outcome MeSH
- Fibromuscular Dysplasia complications pathology MeSH
- Humans MeSH
- Moyamoya Disease complications diagnostic imaging pathology surgery MeSH
- Cerebral Angiography MeSH
- Autopsy MeSH
- Check Tag
- Adult MeSH
- Humans MeSH
- Female MeSH
- Publication type
- Journal Article MeSH
- Case Reports MeSH
A case is reported of a 40-year-old woman clinically diagnosed as moyamoya disease with associated fibromuscular dysplasia of intrapulmonary bronchial arteries incidentally revealed during autoptic examination. Moyamoya disease represents an idiopathic noninflammatory and nonatherosclerotic arterio-occlusive process of intracranial arteries. Prolonged brain ischemia leads to formation of tiny and fragile collaterals. Clinically, patients with moyamoya angiopathy commonly present with severe neurological symptoms caused by brain infarction or hemorrhage. Histologically, the steno-occlusive process is based on fibrocellular thickening of intima and intimal smooth muscle cell proliferation. In the literature, extracranial arterial involvement, i.e. fibromuscular dysplasia of renal or pulmonary arteries, has been described in several cases of moyamoya disease. Our aim is to show a unique case of moyamoya disease associated with fibromuscular dysplasia affecting an uncommon site.
References provided by Crossref.org
