Livedoid Vasculopathy [livedoidní vaskulopatie]

topical
Terms

atrophia blanche
bílá atrofie
idiopatická bílá atrofie
livedo reticularis s letními ulceracemi
livedo vasculitis
livedo vaskulopatie
livedoidní vaskulitida

 

Idiopathic Atrophic Blanche
Livedo Reticularis with Summer Ulceration
Livedo Vasculitis
Livedoid Vasculitis
White Atrophy

Definition

A rare cutaneous thrombotic disease due to occlusion of dermal vessels. It is characterized by purpuric maculae and ulcerations especially during summer which form scars called atrophie blanche. It is more associated with other syndromes (e.g., PROTEIN C DEFICIENCY; HYPERHOMOCYSTEINEMIA). Livedo reticularis with systemic involvement and stroke is SNEDDON SYNDROME.

DUI
D000090122 MeSH Browser
CUI
M000745547
Previous indexing
Skin Diseases, Vascular (1998-2021)
History note
2022
Public note
2022

C Diseases
C14.907 Vascular Diseases 1 790
C14.907.355.830 Thrombosis 1 664
C14.907.355.830.220 Coronary Thrombosis 167
C14.907.355.830.573 Livedoid Vasculopathy
C14.907.355.830.573.500 Livedo Reticularis 14
C14.907.355.830.573.750 Raynaud Disease 193
C14.907.355.830.749 Thromboinflammation 3
C14.907.355.830.925 Venous Thrombosis 1 101
C17.800 Skin Diseases 2 799
C17.800.862.060 Angiomatosis, Bacillary 5
C17.800.862.150 Behcet Syndrome 56
C17.800.862.201 Cryoglobulinemia 72
C17.800.862.252 Giant Cell Arteritis 138
C17.800.862.329 IgA Vasculitis 76
C17.800.862.406 Livedoid Vasculopathy
C17.800.862.406.500 Livedo Reticularis 14
C17.800.862.406.750 Raynaud Disease 193
C17.800.862.625 Polyarteritis Nodosa 92
C17.800.862.675 Pyoderma Gangrenosum 77
C17.800.862.775 Sneddon Syndrome 2
C17.800.862.875 Takayasu Arteritis 93
C17.800.862.945 Urticaria 299