komplement C3 nefritický faktor [Complement C3 Nephritic Factor]

tematický
3
Termíny

komplement 3 nefritický faktor

 

C 3 Nephritic Factor
C3 NeF
C3 NeF IgG Autoantibodies
C3 NeF IgG Autoantibody
C3 Nephritic Factor
C3NeF IgG Autoantibodies
C3NeF IgG Autoantibody
Complement 3 Nephritic Factor

Perzistentní odkaz   https://www.medvik.cz/link/D003178
Definice

An IgG autoantibody against the ALTERNATIVE PATHWAY C3 CONVERTASE, found in serum of patients with MESANGIOCAPILLARY GLOMERULONEPHRITIS. The binding of this autoantibody to C3bBb stabilizes the enzyme thus reduces the actions of C3b inactivators (COMPLEMENT FACTOR H; COMPLEMENT FACTOR I). This abnormally stabilized enzyme induces a continuous COMPLEMENT ACTIVATION and generation of C3b thereby promoting the assembly of MEMBRANE ATTACK COMPLEX and cytolysis.

DUI
D003178 MeSH Prohlížeč
CUI
M0004930
Předchozí užití
Blood Proteins (1966-1977); Complement 3 (1975-1977)
Historická pozn.
2006 (1978)
Veřejná pozn.
2006; see COMPLEMENT 3 NEPHRITIC FACTOR 1991-2005, see COMPLEMENT INACTIVATORS 1978-1990

D Chemikálie a léčiva
D12.776 proteiny 2 575
D12.776.124 krevní proteiny 909
D12.776.124.486 imunoproteiny 14
D12.776.124.486.274 komplement 351
D12.776.124.486.274.920 inaktivátory komplementu 21
D12.776.124.486.274.920.124 antigeny CD46 4
D12.776.124.486.274.920.250 komplement C1 - inaktivátory 9
D12.776.124.486.274.920.287 komplement C3 nefritický faktor 3
D12.776.124.486.274.920.325 komplement C3b - inaktivátory 2
D12.776.124.486.274.920.662 protein vázající komplement C4b
D12.776.124.486.485 imunoglobuliny 1 486
D12.776.124.486.485.114 protilátky 1 815
D12.776.124.486.485.114.323 autoprotilátky 1 321
D12.776.124.486.485.114.323.095 protilátky proti citrulinovaným peptidům 11
D12.776.124.486.485.114.323.190 protilátky proti cytoplazmě neutrofilů 156
D12.776.124.486.485.114.323.204 antinukleární protilátky 142
D12.776.124.486.485.114.323.210 antifosfolipidové protilátky 166
D12.776.124.486.485.114.323.300 komplement C3 nefritický faktor 3
D12.776.124.486.485.114.323.390 imunokonglutininy 1
D12.776.124.486.485.114.323.480 imunoglobuliny stimulující tyreoideu 19
D12.776.124.486.485.114.323.732 revmatoidní faktor 113
D12.776.124.790 sérové globuliny 61
D12.776.124.790.651 imunoglobuliny 1 486
D12.776.124.790.651.114 protilátky 1 815
D12.776.124.790.651.114.323 autoprotilátky 1 321
D12.776.124.790.651.114.323.095 protilátky proti citrulinovaným peptidům 11
D12.776.124.790.651.114.323.190 protilátky proti cytoplazmě neutrofilů 156
D12.776.124.790.651.114.323.204 antinukleární protilátky 142
D12.776.124.790.651.114.323.210 antifosfolipidové protilátky 166
D12.776.124.790.651.114.323.300 komplement C3 nefritický faktor 3
D12.776.124.790.651.114.323.390 imunokonglutininy 1
D12.776.124.790.651.114.323.480 imunoglobuliny stimulující tyreoideu 19
D12.776.124.790.651.114.323.732 revmatoidní faktor 113
D12.776.377 globuliny 68
D12.776.377.715 sérové globuliny 61
D12.776.377.715.548 imunoglobuliny 1 486
D12.776.377.715.548.114 protilátky 1 815
D12.776.377.715.548.114.323 autoprotilátky 1 321
D12.776.377.715.548.114.323.095 protilátky proti citrulinovaným peptidům 11
D12.776.377.715.548.114.323.190 protilátky proti cytoplazmě neutrofilů 156
D12.776.377.715.548.114.323.204 antinukleární protilátky 142
D12.776.377.715.548.114.323.210 antifosfolipidové protilátky 166
D12.776.377.715.548.114.323.300 komplement C3 nefritický faktor 3
D12.776.377.715.548.114.323.390 imunokonglutininy 1
D12.776.377.715.548.114.323.480 imunoglobuliny stimulující tyreoideu 19
D12.776.377.715.548.114.323.732 revmatoidní faktor 113