Cystinuria [cystinurie]

topical
45
Persistent link   https://www.medvik.cz/link/D003555
Definition

An inherited disorder due to defective reabsorption of CYSTINE and other BASIC AMINO ACIDS by the PROXIMAL RENAL TUBULES. This form of aminoaciduria is characterized by the abnormally high urinary levels of cystine; LYSINE; ARGININE; and ORNITHINE. Mutations involve the amino acid transport protein gene SLC3A1.

DUI
D003555 MeSH Browser
CUI
M0005557

C Diseases
C12.050.351.968 Urologic Diseases 834
C12.050.351.968.419 Kidney Diseases 3 059
C12.050.351.968.419.815 Renal Tubular Transport, Inborn Errors 36
C12.050.351.968.419.815.885 Renal Aminoacidurias 27
C12.050.351.968.419.815.885.250 Cystinuria 45
C12.050.351.968.419.815.885.625 Hartnup Disease 2
C12.200.777 Urologic Diseases 834
C12.200.777.419 Kidney Diseases 3 059
C12.200.777.419.815.885 Renal Aminoacidurias 27
C12.200.777.419.815.885.250 Cystinuria 45
C12.200.777.419.815.885.457 Hartnup Disease 2
C12.950.419 Kidney Diseases 3 059
C12.950.419.815.885 Renal Aminoacidurias 27
C12.950.419.815.885.250 Cystinuria 45
C12.950.419.815.885.625 Hartnup Disease 2
C16.320.831.885 Renal Aminoacidurias 27
C16.320.831.885.250 Cystinuria 45
C16.320.831.885.457 Hartnup Disease 2