Lymphangiomyoma [lymfangiomyom]

topical
1
Terms

Lymphangioleiomyoma

Persistent link   https://www.medvik.cz/link/D008203
Definition

A tumorlike condition characterized by SMOOTH MUSCLE and ENDOTHELIUM proliferation of LYMPHATIC VESSELS and LYMPH NODES in the MEDIASTINUM and retroperitoneum, also in the lung. It may be manifested by chylous PLEURAL EFFUSION and ASCITES.

Annotation
differentiate from LYMPHANGIOMYOMATOSIS; coordinate IM with precoordinated organ/neoplasm terms (IM)
DUI
D008203 MeSH Browser
CUI
M0012789
Previous indexing
Lymphangioma (1966-1979); Lymphatic Diseases (1968-1979)
History note
91(80); was see under LYMPHOPROLIFERATIVE DISORDERS 1980-90
Public note
91; was see under LYMPHOPROLIFERATIVE DISORDERS 1980-90

C Diseases
C04 Neoplasms 12 774
C04.557.375.450 Lymphangioma 60
C04.557.375.460 Lymphangiomyoma 1
C04.557.375.460.465 Lymphangioleiomyomatosis 31
C04.557.375.480 Lymphangiosarcoma 8
C15.604.515.032 Agammaglobulinemia 113
C15.604.515.245 Castleman Disease 61
C15.604.515.292 Granuloma 236
C15.604.515.435 Heavy Chain Disease 8
C15.604.515.516 Infectious Mononucleosis 191
C15.604.515.553 Leukemia, Hairy Cell 95
C15.604.515.560 Leukemia, Lymphoid 477
C15.604.515.562 Lymphangiomyoma 1
C15.604.515.562.465 Lymphangioleiomyomatosis 31
C15.604.515.569 Lymphoma 1 119
C15.604.515.700 Marek Disease 7
C15.604.515.827 Sarcoidosis 500
C15.604.515.841 Sezary Syndrome 43
C15.604.515.880 Tumor Lysis Syndrome 38
C20.683.515.250 Castleman Disease 61
C20.683.515.515 Infectious Mononucleosis 191
C20.683.515.517 Leukemia, Hairy Cell 95
C20.683.515.528 Leukemia, Lymphoid 477
C20.683.515.710 Lymphangiomyoma 1
C20.683.515.710.465 Lymphangioleiomyomatosis 31
C20.683.515.761 Lymphoma 1 119
C20.683.515.840 Marek Disease 7
C20.683.515.845 Multiple Myeloma 1 782
C20.683.515.880 Plasmacytoma 179
C20.683.515.920 Sezary Syndrome 43
C20.683.515.950 Tumor Lysis Syndrome 38