Phenylalanine Hydroxylase [fenylalaninhydroxylasa]
- Terms
-
fenylalanin-4-monooxygenasa
fenylalanin-4-monooxygenáza
fenylalaninhydroxyláza
-
Phenylalanine 4-Hydroxylase
Phenylalanine 4-Monooxygenase
An enzyme of the oxidoreductase class that catalyzes the formation of L-TYROSINE, dihydrobiopterin, and water from L-PHENYLALANINE, tetrahydrobiopterin, and oxygen. Deficiency of this enzyme may cause PHENYLKETONURIAS and PHENYLKETONURIA, MATERNAL. EC 1.14.16.1.
- Annotation
- /defic: consider also PHENYLKETONURIAS and PHENYLKETONURIA, MATERNAL
- DUI
- D010651 MeSH Browser
- CUI
- M0016546
- CAS
- L-Phenylalanine,tetrahydrobiopterin:oxygen oxidoreductase (4-hydroxylating)
- Previous indexing
- Hydroxylases (1966-1970)
- History note
- 73(71)
- Public note
- 73
Allowable subheadings
- AD
- administration & dosage
- AE
- adverse effects
- AN
- analysis 2
- AI
- antagonists & inhibitors
- BI
- biosynthesis
- BL
- blood 1
- CF
- cerebrospinal fluid
- CS
- chemical synthesis
- CH
- chemistry 1
- CL
- classification
- DF
- deficiency 4
- DE
- drug effects
- EC
- economics
- GE
- genetics 15
- HI
- history
- IM
- immunology
- IP
- isolation & purification
- ME
- metabolism 5
- PK
- pharmacokinetics
- PD
- pharmacology
- PH
- physiology
- PO
- poisoning
- RE
- radiation effects
- ST
- standards
- SD
- supply & distribution
- TU
- therapeutic use
- TO
- toxicity
- UL
- ultrastructure
- UR
- urine