Purpura, Thrombotic Thrombocytopenic [trombotická trombocytopenická purpura]
- Terms
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familiární trombotická trombocytopenická purpura
Moschcowitzova choroba
Moschcowitzova nemoc
Moschkowitzova choroba
purpura trombotická trombocytopenická
Upshawův-Schulmanův syndrom
vrozená forma trombotické trombocytopenické purpury
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Congenital Thrombotic Thrombocytopenic Purpura
Familial Thrombotic Thrombocytopenia Purpura
Familial Thrombotic Thrombocytopenic Purpura
Microangiopathic Hemolytic Anemia, Congenital
Moschcowitz Disease
Moschkowitz Disease
Purpura, Thrombotic Thrombopenic
Schulman-Upshaw Syndrome
Thrombotic Microangiopathy, Familial
Thrombotic Thrombocytopenic Purpura
Thrombotic Thrombocytopenic Purpura, Congenital
Thrombotic Thrombocytopenic Purpura, Familial
Upshaw Factor, Deficiency of
Upshaw-Schulman Syndrome
An acquired, congenital, or familial disorder caused by PLATELET AGGREGATION with THROMBOSIS in terminal arterioles and capillaries. Clinical features include THROMBOCYTOPENIA; HEMOLYTIC ANEMIA; AZOTEMIA; FEVER; and thrombotic microangiopathy. The classical form also includes neurological symptoms and end-organ damage, such as RENAL FAILURE. Mutations in the ADAMTS13 PROTEIN gene have been identified in familial cases.
- DUI
- D011697 MeSH Browser
- CUI
- M0018188
- History note
- 1986; use PURPURA, THROMBOTIC THROMBOPENIC 1965-1985
- Public note
- 1986; see PURPURA, THROMBOTIC THROMBOPENIC 1965-1985
Allowable subheadings
- BL
- blood 7
- CF
- cerebrospinal fluid
- CI
- chemically induced
- CL
- classification
- CO
- complications 7
- CN
- congenital 4
- DI
- diagnosis 45
- DG
- diagnostic imaging
- DH
- diet therapy
- DT
- drug therapy 8
- EC
- economics
- EM
- embryology
- EN
- enzymology 2
- EP
- epidemiology 5
- EH
- ethnology
- ET
- etiology 28
- GE
- genetics 3
- HI
- history
- IM
- immunology 2
- ME
- metabolism 1
- MI
- microbiology 1
- MO
- mortality 1
- NU
- nursing 2
- PS
- parasitology
- PA
- pathology 12
- PP
- physiopathology 12
- PC
- prevention & control 3
- PX
- psychology
- RT
- radiotherapy
- RH
- rehabilitation
- SU
- surgery 1
- TH
- therapy 54
- UR
- urine
- VE
- veterinary
- VI
- virology
Thrombotic thrombocytopenic purpura, acquired Disease MeSH Browser