Protein S Deficiency [nedostatek proteinu S]

topical
18
Terms

deficience proteinu S
deficit proteinu S
protein S - nedostatek

 

Deficiency, Protein S
Hereditary Thrombophilia Due To Protein S Deficiency

Persistent link   https://www.medvik.cz/link/D018455
Definition

An autosomal dominant disorder showing decreased levels of plasma protein S antigen or activity, associated with venous thrombosis and pulmonary embolism. PROTEIN S is a vitamin K-dependent plasma protein that inhibits blood clotting by serving as a cofactor for activated PROTEIN C (also a vitamin K-dependent protein), and the clinical manifestations of its deficiency are virtually identical to those of protein C deficiency. Treatment with heparin for acute thrombotic processes is usually followed by maintenance administration of coumarin drugs for the prevention of recurrent thrombosis. (From Harrison's Principles of Internal Medicine, 12th ed, p1511; Wintrobe's Clinical Hematology, 9th ed, p1523)

DUI
D018455 MeSH Browser
CUI
M0027690
Previous indexing
Glycoproteins/deficiency (1984-1992); Protein S/deficiency (1993-1994)
History note
95
Public note
95

C Diseases
C15.378.100.452 Ecchymosis 10
C15.378.100.800 Protein S Deficiency 18
C15.378.100.802 Purpura 109
C15.378.100.832 Thrombocythemia, Essential 94
C15.378.100.876 Thromboinflammation 3
C15.378.100.920 Vitamin K Deficiency 42
C15.378.147.142 Agammaglobulinemia 113
C15.378.147.333 Dysgammaglobulinemia 10
C15.378.147.542 Hypergammaglobulinemia 55
C15.378.147.607 Hypoproteinemia 27
C15.378.147.780 Paraproteinemias 289
C15.378.147.880 Protein C Deficiency 31
C15.378.147.890 Protein S Deficiency 18
C15.378.925 Thrombophilia 424
C15.378.925.795 Protein C Deficiency 31
C15.378.925.800 Protein S Deficiency 18

Acquired Protein S Deficiency Disease MeSH Browser

Thrombophilia, Hereditary, Due To Protein S Deficiency, Autosomal Dominant Disease MeSH Browser

Thrombophilia, Hereditary, Due To Protein S Deficiency, Autosomal Recessive Disease MeSH Browser