nedostatek proteinu C [Protein C Deficiency]

tematický
31
Termíny

deficit proteinu C
protein C - nedostatek

 

Deficiency, Protein C
Hereditary Thrombophilia Due To Protein C Deficiency

Perzistentní odkaz   https://www.medvik.cz/link/D020151
Definice

Chybění nebo deficit proteinu C vede k poruše regulace krevní koagulace. Souvisí se zvýšeným rizikem těžké nebo časné trombózy.

An absence or deficiency in PROTEIN C which leads to impaired regulation of blood coagulation. It is associated with an increased risk of severe or premature thrombosis. (Stedman's Med. Dict., 26th ed.)

DUI
D020151 MeSH Prohlížeč
CUI
M0029882
Předchozí užití
Blood Proteins (1981-1987); Glycoproteins (1981-1987); Protein C (1987-1998)
Historická pozn.
1999
Veřejná pozn.
1999

C Nemoci
C15.378 krevní nemoci 973
C15.378.100 koagulopatie 599
C15.378.100.100 dědičné koagulopatie 61
C15.378.100.100.056 afibrinogenemie 39
C15.378.100.100.075 nedostatek antitrombinu III 24
C15.378.100.100.080 Bernardův-Soulierův syndrom 9
C15.378.100.100.300 nedostatek faktoru V 7
C15.378.100.100.310 nedostatek faktoru VII 6
C15.378.100.100.320 nedostatek faktoru X 2
C15.378.100.100.325 nedostatek faktoru XI 12
C15.378.100.100.330 nedostatek faktoru XII 8
C15.378.100.100.335 nedostatek faktoru XIII 4
C15.378.100.100.500 hemofilie A 688
C15.378.100.100.510 hemofilie B 214
C15.378.100.100.550 hypoprotrombinemie 4
C15.378.100.100.690 nedostatek proteinu C 31
C15.378.100.100.820 trombastenie 7
C15.378.100.100.900 von Willebrandova nemoc 103
C15.378.100.100.970 Wiskottův-Aldrichův syndrom 20
C15.378.147.142 agamaglobulinemie 113
C15.378.147.333 dysgamaglobulinemie 10
C15.378.147.542 hypergamaglobulinemie 55
C15.378.147.607 hypoproteinemie 27
C15.378.147.780 paraproteinemie 285
C15.378.147.880 nedostatek proteinu C 31
C15.378.147.890 nedostatek proteinu S 18
C15.378.925 trombofilie 424
C15.378.925.795 nedostatek proteinu C 31
C15.378.925.800 nedostatek proteinu S 18
C16.320.099.056 afibrinogenemie 39
C16.320.099.300 nedostatek faktoru V 7
C16.320.099.310 nedostatek faktoru VII 6
C16.320.099.320 nedostatek faktoru X 2
C16.320.099.325 nedostatek faktoru XI 12
C16.320.099.330 nedostatek faktoru XII 8
C16.320.099.335 nedostatek faktoru XIII 4
C16.320.099.500 hemofilie A 688
C16.320.099.510 hemofilie B 214
C16.320.099.550 hypoprotrombinemie 4
C16.320.099.690 nedostatek proteinu C 31
C16.320.099.820 trombastenie 7
C16.320.099.920 von Willebrandova nemoc 103