Bernard-Soulier Syndrome [Bernardův-Soulierův syndrom]
- Terms
-
deficit trombocytárního glykoproteinového komplexu gpIb-IX
syndrom obrovských destiček
trombocytopatie s obrovskými destičkami typu Soulier-Bernard
-
Deficiency of Platelet Glycoprotein 1b
Giant Platelet Syndrome
Glycoprotein Ib, Platelet, Deficiency Of
Platelet Glycoprotein 1b, Deficiency of
Platelet Glycoprotein Ib Deficiency
Von Willebrand Factor Receptor Deficiency
A familial coagulation disorder characterized by a prolonged bleeding time, unusually large platelets, and impaired prothrombin consumption.
- DUI
- D001606 MeSH Browser
- CUI
- M0002403
- Previous indexing
- Blood Platelet Disorders (1967-1985)
- History note
- 1991(1986)
- Public note
- 1991; see BLOOD PLATELET DISORDERS 1986-1990
Allowable subheadings
- BL
- blood 1
- CF
- cerebrospinal fluid
- CI
- chemically induced
- CL
- classification
- CO
- complications
- DI
- diagnosis 5
- DG
- diagnostic imaging
- DH
- diet therapy
- DT
- drug therapy
- EC
- economics
- EM
- embryology
- EN
- enzymology
- EP
- epidemiology
- EH
- ethnology
- ET
- etiology 1
- GE
- genetics 3
- HI
- history
- IM
- immunology
- ME
- metabolism 1
- MI
- microbiology
- MO
- mortality
- NU
- nursing
- PS
- parasitology
- PA
- pathology
- PP
- physiopathology
- PC
- prevention & control
- PX
- psychology
- RT
- radiotherapy
- RH
- rehabilitation
- SU
- surgery
- TH
- therapy 2
- UR
- urine
- VE
- veterinary 1
- VI
- virology
Bernard-Soulier Syndrome, Autosomal Dominant Disease MeSH Browser
Bernard-Soulier Syndrome, Type A Disease MeSH Browser
Bernard-Soulier Syndrome, Type B Disease MeSH Browser
Bernard-Soulier Syndrome, Type C Disease MeSH Browser