Factor V Deficiency [nedostatek faktoru V]

topical
7
Terms

deficit koagulačního faktoru V
faktor V - nedostatek
Owrenova parahemofilie
Owrenův syndrom
parahemofilie

 

Deficiency, Factor 5
Deficiency, Factor Five
Deficiency, Factor V
Factor 5 Deficiency
Factor Five Deficiency
Labile Factor Deficiency
Owren Disease
Owren Parahemophilia
Owren's Disease
Parahemophilia

Persistent link   https://www.medvik.cz/link/D005166
Definition

A deficiency of blood coagulation factor V (known as proaccelerin or accelerator globulin or labile factor) leading to a rare hemorrhagic tendency known as Owren's disease or parahemophilia. It varies greatly in severity. Factor V deficiency is an autosomal recessive trait. (Dorland, 27th ed)

Annotation
a blood coag disord
DUI
D005166 MeSH Browser
CUI
M0008143
History note
73(64); was see under HYPOPROTHROMBINEMIAS 1963-72
Online note
use HYPOPROTHROMBINEMIAS to search FACTOR V DEFICIENCY 1966-72
Public note
73; was see under HYPOPROTHROMBINEMIAS 1963-72

C Diseases
C15.378.100.100.037 Activated Protein C Resistance 105
C15.378.100.100.056 Afibrinogenemia 39
C15.378.100.100.075 Antithrombin III Deficiency 24
C15.378.100.100.080 Bernard-Soulier Syndrome 9
C15.378.100.100.300 Factor V Deficiency 7
C15.378.100.100.310 Factor VII Deficiency 6
C15.378.100.100.320 Factor X Deficiency 2
C15.378.100.100.325 Factor XI Deficiency 12
C15.378.100.100.330 Factor XII Deficiency 8
C15.378.100.100.335 Factor XIII Deficiency 4
C15.378.100.100.500 Hemophilia A 688
C15.378.100.100.510 Hemophilia B 214
C15.378.100.100.515 Hermanski-Pudlak Syndrome 7
C15.378.100.100.550 Hypoprothrombinemias 4
C15.378.100.100.690 Protein C Deficiency 31
C15.378.100.100.820 Thrombasthenia 7
C15.378.100.100.900 von Willebrand Diseases 103
C15.378.100.100.970 Wiskott-Aldrich Syndrome 20
C15.378.100.141.036 Activated Protein C Resistance 105
C15.378.100.141.072 Afibrinogenemia 39
C15.378.100.141.300 Factor V Deficiency 7
C15.378.100.141.310 Factor VII Deficiency 6
C15.378.100.141.320 Factor X Deficiency 2
C15.378.100.141.325 Factor XI Deficiency 12
C15.378.100.141.330 Factor XII Deficiency 8
C15.378.100.141.335 Factor XIII Deficiency 4
C15.378.100.141.500 Hemophilia A 688
C15.378.100.141.510 Hemophilia B 214
C15.378.100.141.550 Hypoprothrombinemias 4
C15.378.100.141.900 von Willebrand Diseases 103
C15.378.463.067 Afibrinogenemia 39
C15.378.463.080 Bernard-Soulier Syndrome 9
C15.378.463.300 Factor V Deficiency 7
C15.378.463.310 Factor VII Deficiency 6
C15.378.463.320 Factor X Deficiency 2
C15.378.463.325 Factor XI Deficiency 12
C15.378.463.330 Factor XII Deficiency 8
C15.378.463.335 Factor XIII Deficiency 4
C15.378.463.500 Hemophilia A 688
C15.378.463.510 Hemophilia B 214
C15.378.463.515 Hemostatic Disorders 49
C15.378.463.550 Hypoprothrombinemias 4
C15.378.463.810 Thrombasthenia 7
C15.378.463.825 Thrombocythemia, Essential 94
C15.378.463.841 Vitamin K Deficiency 42
C15.378.463.920 von Willebrand Diseases 103
C15.378.463.960 Wiskott-Aldrich Syndrome 20
C16.320.099.056 Afibrinogenemia 39
C16.320.099.080 Bernard-Soulier Syndrome 9
C16.320.099.300 Factor V Deficiency 7
C16.320.099.310 Factor VII Deficiency 6
C16.320.099.320 Factor X Deficiency 2
C16.320.099.325 Factor XI Deficiency 12
C16.320.099.330 Factor XII Deficiency 8
C16.320.099.335 Factor XIII Deficiency 4
C16.320.099.417 Gray Platelet Syndrome 1
C16.320.099.500 Hemophilia A 688
C16.320.099.510 Hemophilia B 214
C16.320.099.515 Hermanski-Pudlak Syndrome 7
C16.320.099.550 Hypoprothrombinemias 4
C16.320.099.690 Protein C Deficiency 31
C16.320.099.820 Thrombasthenia 7
C16.320.099.920 von Willebrand Diseases 103
C16.320.099.970 Wiskott-Aldrich Syndrome 20

Familial Multiple Coagulation Factor Deficiency I Disease MeSH Browser

Quebec platelet disorder Disease MeSH Browser