nedostatek faktoru X [Factor X Deficiency]

tematický
2
Termíny

deficience faktoru X
deficience Stuartova-Prowerové
deficit faktoru Stuartova-Prowerové
deficit faktoru X
deficit koagulačního faktoru X
faktor X - nedostatek

 

Deficiency, Factor 10
Deficiency, Factor Ten
Deficiency, Factor X
Deficiency, Stuart-Prower
Deficiency, Stuart-Prower Factor
Factor 10 Deficiency
Factor Ten Deficiency
Stuart-Prower Deficiency
Stuart-Prower Factor Deficiency

Perzistentní odkaz   https://www.medvik.cz/link/D005171
Definice

Porucha krevní koagulace, zpravidla autozomálně recesivně dědičná, ale může být i získaná. Je charakterizovaná poruchou aktivity vnitřního i zevního systému koagulace, zhoršenou hodnotou tromboplastinového času a poruchou přeměny protrombinu.

Blood coagulation disorder usually inherited as an autosomal recessive trait, though it can be acquired. It is characterized by defective activity in both the intrinsic and extrinsic pathways, impaired thromboplastin time, and impaired prothrombin consumption.

Anotace
a blood coag disord
DUI
D005171 MeSH Prohlížeč
CUI
M0008155
Historická pozn.
91(75); was see under HYPOPROTHROMBINEMIAS 1975-90
Online pozn.
search HYPOPROTHROMBINEMIAS 1966-74
Veřejná pozn.
91; was see under HYPOPROTHROMBINEMIAS 1975-90

C Nemoci
C15.378 krevní nemoci 973
C15.378.100 koagulopatie 599
C15.378.100.100 dědičné koagulopatie 61
C15.378.100.100.056 afibrinogenemie 39
C15.378.100.100.075 nedostatek antitrombinu III 24
C15.378.100.100.080 Bernardův-Soulierův syndrom 9
C15.378.100.100.300 nedostatek faktoru V 7
C15.378.100.100.310 nedostatek faktoru VII 6
C15.378.100.100.320 nedostatek faktoru X 2
C15.378.100.100.325 nedostatek faktoru XI 12
C15.378.100.100.330 nedostatek faktoru XII 8
C15.378.100.100.335 nedostatek faktoru XIII 4
C15.378.100.100.500 hemofilie A 688
C15.378.100.100.510 hemofilie B 214
C15.378.100.100.550 hypoprotrombinemie 4
C15.378.100.100.690 nedostatek proteinu C 31
C15.378.100.100.820 trombastenie 7
C15.378.100.100.900 von Willebrandova nemoc 103
C15.378.100.100.970 Wiskottův-Aldrichův syndrom 20
C15.378.100.141.072 afibrinogenemie 39
C15.378.100.141.300 nedostatek faktoru V 7
C15.378.100.141.310 nedostatek faktoru VII 6
C15.378.100.141.320 nedostatek faktoru X 2
C15.378.100.141.325 nedostatek faktoru XI 12
C15.378.100.141.330 nedostatek faktoru XII 8
C15.378.100.141.335 nedostatek faktoru XIII 4
C15.378.100.141.500 hemofilie A 688
C15.378.100.141.510 hemofilie B 214
C15.378.100.141.550 hypoprotrombinemie 4
C15.378.100.141.900 von Willebrandova nemoc 103
C15.378.463 hemoragické poruchy 95
C15.378.463.067 afibrinogenemie 39
C15.378.463.300 nedostatek faktoru V 7
C15.378.463.310 nedostatek faktoru VII 6
C15.378.463.320 nedostatek faktoru X 2
C15.378.463.325 nedostatek faktoru XI 12
C15.378.463.330 nedostatek faktoru XII 8
C15.378.463.335 nedostatek faktoru XIII 4
C15.378.463.500 hemofilie A 688
C15.378.463.510 hemofilie B 214
C15.378.463.515 poruchy hemostázy 49
C15.378.463.550 hypoprotrombinemie 4
C15.378.463.810 trombastenie 7
C15.378.463.825 esenciální trombocytemie 93
C15.378.463.841 nedostatek vitaminu K 42
C15.378.463.920 von Willebrandova nemoc 103
C16.320.099.056 afibrinogenemie 39
C16.320.099.300 nedostatek faktoru V 7
C16.320.099.310 nedostatek faktoru VII 6
C16.320.099.320 nedostatek faktoru X 2
C16.320.099.325 nedostatek faktoru XI 12
C16.320.099.330 nedostatek faktoru XII 8
C16.320.099.335 nedostatek faktoru XIII 4
C16.320.099.500 hemofilie A 688
C16.320.099.510 hemofilie B 214
C16.320.099.550 hypoprotrombinemie 4
C16.320.099.690 nedostatek proteinu C 31
C16.320.099.820 trombastenie 7
C16.320.099.920 von Willebrandova nemoc 103