Factor XI Deficiency [nedostatek faktoru XI]

topical
12
Terms

deficit koagulačního faktoru XI
faktor XI - nedostatek
hemofilie C (starší název)

 

Deficiency, Factor 11
Deficiency, Factor Eleven
Deficiency, Factor XI
Factor 11 Deficiency
Factor Eleven Deficiency
Hemophilia C
Plasma Thromboplastin Antecedent Deficiency
Rosenthal Syndrome
Rosenthal's Syndrome

Persistent link   https://www.medvik.cz/link/D005173
Definition

A hereditary deficiency of blood coagulation factor XI (also known as plasma thromboplastin antecedent or PTA or antihemophilic factor C) resulting in a systemic blood-clotting defect called hemophilia C or Rosenthal's syndrome, that may resemble classical hemophilia.

Annotation
a blood coag disord
DUI
D005173 MeSH Browser
CUI
M0008157
History note
1973(1966)
Public note
1973

C Diseases
C15.378.100.100.037 Activated Protein C Resistance 105
C15.378.100.100.056 Afibrinogenemia 39
C15.378.100.100.075 Antithrombin III Deficiency 24
C15.378.100.100.080 Bernard-Soulier Syndrome 9
C15.378.100.100.300 Factor V Deficiency 7
C15.378.100.100.310 Factor VII Deficiency 6
C15.378.100.100.320 Factor X Deficiency 2
C15.378.100.100.325 Factor XI Deficiency 12
C15.378.100.100.330 Factor XII Deficiency 8
C15.378.100.100.335 Factor XIII Deficiency 4
C15.378.100.100.500 Hemophilia A 691
C15.378.100.100.510 Hemophilia B 216
C15.378.100.100.515 Hermanski-Pudlak Syndrome 7
C15.378.100.100.550 Hypoprothrombinemias 4
C15.378.100.100.690 Protein C Deficiency 31
C15.378.100.100.820 Thrombasthenia 7
C15.378.100.100.900 von Willebrand Diseases 103
C15.378.100.100.970 Wiskott-Aldrich Syndrome 20
C15.378.100.141.036 Activated Protein C Resistance 105
C15.378.100.141.072 Afibrinogenemia 39
C15.378.100.141.300 Factor V Deficiency 7
C15.378.100.141.310 Factor VII Deficiency 6
C15.378.100.141.320 Factor X Deficiency 2
C15.378.100.141.325 Factor XI Deficiency 12
C15.378.100.141.330 Factor XII Deficiency 8
C15.378.100.141.335 Factor XIII Deficiency 4
C15.378.100.141.500 Hemophilia A 691
C15.378.100.141.510 Hemophilia B 216
C15.378.100.141.550 Hypoprothrombinemias 4
C15.378.100.141.900 von Willebrand Diseases 103
C15.378.463.067 Afibrinogenemia 39
C15.378.463.080 Bernard-Soulier Syndrome 9
C15.378.463.300 Factor V Deficiency 7
C15.378.463.310 Factor VII Deficiency 6
C15.378.463.320 Factor X Deficiency 2
C15.378.463.325 Factor XI Deficiency 12
C15.378.463.330 Factor XII Deficiency 8
C15.378.463.335 Factor XIII Deficiency 4
C15.378.463.500 Hemophilia A 691
C15.378.463.510 Hemophilia B 216
C15.378.463.515 Hemostatic Disorders 49
C15.378.463.550 Hypoprothrombinemias 4
C15.378.463.810 Thrombasthenia 7
C15.378.463.825 Thrombocythemia, Essential 94
C15.378.463.841 Vitamin K Deficiency 42
C15.378.463.920 von Willebrand Diseases 103
C15.378.463.960 Wiskott-Aldrich Syndrome 20
C16.320.099.056 Afibrinogenemia 39
C16.320.099.080 Bernard-Soulier Syndrome 9
C16.320.099.300 Factor V Deficiency 7
C16.320.099.310 Factor VII Deficiency 6
C16.320.099.320 Factor X Deficiency 2
C16.320.099.325 Factor XI Deficiency 12
C16.320.099.330 Factor XII Deficiency 8
C16.320.099.335 Factor XIII Deficiency 4
C16.320.099.417 Gray Platelet Syndrome 1
C16.320.099.500 Hemophilia A 691
C16.320.099.510 Hemophilia B 216
C16.320.099.515 Hermanski-Pudlak Syndrome 7
C16.320.099.550 Hypoprothrombinemias 4
C16.320.099.690 Protein C Deficiency 31
C16.320.099.820 Thrombasthenia 7
C16.320.099.920 von Willebrand Diseases 103
C16.320.099.970 Wiskott-Aldrich Syndrome 20