epidermolysis bullosa simplex [Epidermolysis Bullosa Simplex]

tematický
14
Termíny

EBS-DM
epidermolysis bullosa simplex, Köbnerův typ
epidermolysis bullosa simplex, typ Dowling-Meara
generalizovaná EBS
generalizovaná epidermolysis bullosa simplex
Weber-Cockaynův syndrom
Weberův-Cockayneův syndrom

 

EBS-DM
EBS, Acral Form
EBS, Generalized
Epidermolysis Bullosa Herpetiformis Dowling Meara
Epidermolysis Bullosa Herpetiformis Dowling-Meara
Epidermolysis Bullosa Herpetiformis, Dowling-Meara
Epidermolysis Bullosa Herpetiformis, Dowling-Meara Type
Epidermolysis Bullosa of Hands and Feet
Epidermolysis Bullosa Simplex Kobner
Epidermolysis Bullosa Simplex, Cockayne-Touraine Type
Epidermolysis Bullosa Simplex, Dowling-Meara Type
Epidermolysis Bullosa Simplex, Generalized
Epidermolysis Bullosa Simplex, Koebner Type
Epidermolysis Bullosa Simplex, Localized
Epidermolysis Bullosa Simplex, Weber-Cockayne Type
Weber-Cockayne Syndrome
Weber-Cockayne Type Epidermolysis Bullosa Simplex

Perzistentní odkaz   https://www.medvik.cz/link/D016110
Definice

Forma epidermolysis bullosa charakterizovaná serózními puchýři, které se hojí bez zanechání jizev. Několik podtypů tohoto onemocnění je způsobené mutacemi genů pro keratin 5 a keratin 14.

A form of epidermolysis bullosa characterized by serous bullae that heal without scarring. Mutations in the genes that encode KERATIN-5 and KERATIN-14 have been associated with several subtypes of epidermolysis bullosa simplex.

DUI
D016110 MeSH Prohlížeč
CUI
M0024607
Předchozí užití
Epidermolysis Bullosa (1966-1990)
Historická pozn.
1991
Veřejná pozn.
1991

C Nemoci
C16.131 vrozené vady 1 740
C16.131.831 kožní abnormality 51
C16.131.831.493 epidermolysis bullosa 108
C16.131.831.493.080 epidermolysis bullosa acquisita 22
C16.131.831.493.170 epidermolysis bullosa junkční 8
C16.131.831.493.180 epidermolysis bullosa simplex 14
C16.320.850.275 epidermolysis bullosa 108
C16.320.850.275.170 epidermolysis bullosa junkční 8
C16.320.850.275.180 epidermolysis bullosa simplex 14
C17.800 kožní nemoci 2 796
C17.800.804 kožní abnormality 51
C17.800.804.493 epidermolysis bullosa 108
C17.800.804.493.080 epidermolysis bullosa acquisita 22
C17.800.804.493.170 epidermolysis bullosa junkční 8
C17.800.804.493.180 epidermolysis bullosa simplex 14
C17.800.827.275 epidermolysis bullosa 108
C17.800.827.275.080 epidermolysis bullosa acquisita 22
C17.800.827.275.170 epidermolysis bullosa junkční 8
C17.800.827.275.180 epidermolysis bullosa simplex 14
C17.800.865.410 epidermolysis bullosa 108
C17.800.865.410.080 epidermolysis bullosa acquisita 22
C17.800.865.410.170 epidermolysis bullosa junkční 8
C17.800.865.410.180 epidermolysis bullosa simplex 14