epidermolysis bullosa simplex [Epidermolysis Bullosa Simplex]

tematický
14
Termíny

EBS-DM
epidermolysis bullosa simplex, Köbnerův typ
epidermolysis bullosa simplex, typ Dowling-Meara
generalizovaná EBS
generalizovaná epidermolysis bullosa simplex
Weber-Cockaynův syndrom
Weberův-Cockayneův syndrom

 

EBS-DM
EBS, Acral Form
EBS, Generalized
Epidermolysis Bullosa Herpetiformis Dowling Meara
Epidermolysis Bullosa Herpetiformis Dowling-Meara
Epidermolysis Bullosa Herpetiformis, Dowling-Meara
Epidermolysis Bullosa Herpetiformis, Dowling-Meara Type
Epidermolysis Bullosa of Hands and Feet
Epidermolysis Bullosa Simplex Kobner
Epidermolysis Bullosa Simplex, Cockayne-Touraine Type
Epidermolysis Bullosa Simplex, Dowling-Meara Type
Epidermolysis Bullosa Simplex, Generalized
Epidermolysis Bullosa Simplex, Koebner Type
Epidermolysis Bullosa Simplex, Localized
Epidermolysis Bullosa Simplex, Weber-Cockayne Type
Weber-Cockayne Syndrome
Weber-Cockayne Type Epidermolysis Bullosa Simplex

Perzistentní odkaz   https://www.medvik.cz/link/D016110
Definice

Forma epidermolysis bullosa charakterizovaná serózními puchýři, které se hojí bez zanechání jizev. Několik podtypů tohoto onemocnění je způsobené mutacemi genů pro keratin 5 a keratin 14.

A form of epidermolysis bullosa characterized by serous bullae that heal without scarring. Mutations in the genes that encode KERATIN-5 and KERATIN-14 have been associated with several subtypes of epidermolysis bullosa simplex.

DUI
D016110 MeSH Prohlížeč
CUI
M0024607
Předchozí užití
Epidermolysis Bullosa (1966-1990)
Historická pozn.
1991
Veřejná pozn.
1991

C Nemoci
C16.131 vrozené vady 1 741
C16.131.831 kožní abnormality 51
C16.131.831.493 epidermolysis bullosa 108
C16.131.831.493.080 epidermolysis bullosa acquisita 22
C16.131.831.493.170 epidermolysis bullosa junkční 8
C16.131.831.493.180 epidermolysis bullosa simplex 14
C16.320.850.275 epidermolysis bullosa 108
C16.320.850.275.170 epidermolysis bullosa junkční 8
C16.320.850.275.180 epidermolysis bullosa simplex 14
C17.800 kožní nemoci 2 799
C17.800.804 kožní abnormality 51
C17.800.804.493 epidermolysis bullosa 108
C17.800.804.493.080 epidermolysis bullosa acquisita 22
C17.800.804.493.170 epidermolysis bullosa junkční 8
C17.800.804.493.180 epidermolysis bullosa simplex 14
C17.800.827.275 epidermolysis bullosa 108
C17.800.827.275.080 epidermolysis bullosa acquisita 22
C17.800.827.275.170 epidermolysis bullosa junkční 8
C17.800.827.275.180 epidermolysis bullosa simplex 14
C17.800.865.410 epidermolysis bullosa 108
C17.800.865.410.080 epidermolysis bullosa acquisita 22
C17.800.865.410.170 epidermolysis bullosa junkční 8
C17.800.865.410.180 epidermolysis bullosa simplex 14

Epidermolysa bullosa simplex and limb girdle muscular dystrophy Disease MeSH Prohlížeč

Epidermolysis Bullosa Simplex Superficialis Disease MeSH Prohlížeč

Epidermolysis Bullosa Simplex With Pyloric Atresia Disease MeSH Prohlížeč

Epidermolysis Bullosa Simplex with Migratory Circinate Erythema Disease MeSH Prohlížeč

Epidermolysis Bullosa Simplex, Autosomal Recessive Disease MeSH Prohlížeč

Epidermolysis bullosa simplex with mottled pigmentation Disease MeSH Prohlížeč

Epidermolysis bullosa simplex, Ogna type Disease MeSH Prohlížeč

Epidermolysis bullosa, late-onset localized junctional, with mental retardation Disease MeSH Prohlížeč