Stiff-Person Syndrome [syndrom celkové ztuhlosti]

topical
14
Terms

dědičná hyperekplexie
familiární hyperekplexie
Moerschův-Woltmannův syndrom
stiff person syndrom
syndrom celkového ztuhnutí

 

Congenital Stiff-Man Syndrome
Congenital Stiff-Person Syndrome
Familial Hyperekplexia
Hereditary Hyperekplexia
Moersch-Woltmann Syndrome
Startle Syndrome
Stiff-Baby Syndrome
Stiff-Man Syndrome
Stiff-Trunk Syndrome
Stiffman Syndrome

Persistent link   https://www.medvik.cz/link/D016750
Definition

A condition characterized by persistent spasms (SPASM) involving multiple muscles, primarily in the lower limbs and trunk. The illness tends to occur in the fourth to sixth decade of life, presenting with intermittent spasms that become continuous. Minor sensory stimuli, such as noise and light touch, precipitate severe spasms. Spasms do not occur during sleep and only rarely involve cranial muscles. Respiration may become impaired in advanced cases. (Adams et al., Principles of Neurology, 6th ed, p1492; Neurology 1998 Jul;51(1):85-93)

DUI
D016750 MeSH Browser
CUI
M0025507
Previous indexing
Neuromuscular Diseases (1972-1991); Autoimmune Diseases (1988-1991); Central Nervous System Diseases (1986-1991); Fibromyalgia (1966-1976); Muscular Diseases (1966-1982)
History note
2000(1992)
Public note
2000; see STIFF-MAN SYNDROME 1992-1999

C Diseases
C10.114.656 Myasthenia Gravis 422
C10.228.854 Spinal Cord Diseases 312
C10.228.854.468 Muscular Atrophy, Spinal 131
C10.228.854.525 Myelitis 54
C10.228.854.583 Pneumorrhachis 1
C10.228.854.761 Spinal Cord Compression 226
C10.228.854.763 Spinal Cord Injuries 824
C10.228.854.765 Spinal Cord Neoplasms 114
C10.228.854.790 Stiff-Person Syndrome 14
C10.228.854.833 Syringomyelia 56
C10.228.854.889 Tabes Dorsalis 19
C10.668.416 Locked-In Syndrome 3
C10.668.467 Motor Neuron Disease 63
C10.668.491 Muscular Diseases 557
C10.668.864 Poliomyelitis 476
C20.111 Autoimmune Diseases 1 940
C20.111.258.500 Myasthenia Gravis 422
C20.111.258.750 Polyradiculoneuropathy 68
C20.111.258.850 Stiff-Person Syndrome 14