Caroli Disease [Caroliho nemoc]

topical
6
Terms

Caroliho syndrom

 

Caroli's Disease
Caroli's Syndrome

Persistent link   https://www.medvik.cz/link/D016767
Definition

Congenital cystic dilatation of the intrahepatic bile ducts (BILE DUCTS, INTRAHEPATIC). It consists of 2 types: simple Caroli disease is characterized by bile duct dilatation (ectasia) alone; and complex Caroli disease is characterized by bile duct dilatation with extensive hepatic fibrosis and portal hypertension (HYPERTENSION, PORTAL). Benign renal tubular ectasia is associated with both types of Caroli disease.

DUI
D016767 MeSH Browser
CUI
M0025558
Previous indexing
Bile Duct Diseases/congenital (1966-1992); Bile Ducts, Intrahepatic/abnormalities (1985-1992); Biliary Dyskinesia (1966-1984)
History note
2004 (1993)
Public note
2004; see CAROLI'S DISEASE 1993-2003

C Diseases
C06.130.120 Bile Duct Diseases 352
C06.130.120.127 Choledochal Cyst 28
C06.130.120.127.500 Caroli Disease 6
C06.198.184 Choledochal Cyst 28
C06.198.184.500 Caroli Disease 6
C16.131.077.245 Ciliopathies 9
C16.131.077.245.063 Alstrom Syndrome 1
C16.131.077.245.125 Bardet-Biedl Syndrome 18
C16.131.077.245.250 Caroli Disease 6
C16.131.077.245.500 Ciliary Motility Disorders 57
C16.131.077.245.750 von Hippel-Lindau Disease 56
C16.131.314.184 Choledochal Cyst 28
C16.131.314.184.500 Caroli Disease 6
C16.320.184 Ciliopathies 9
C16.320.184.063 Alstrom Syndrome 1
C16.320.184.125 Bardet-Biedl Syndrome 18
C16.320.184.250 Caroli Disease 6
C16.320.184.500 Ciliary Motility Disorders 57
C16.320.184.625 Polycystic Kidney Diseases 82
C16.320.184.750 von Hippel-Lindau Disease 56