Sarcosine Dehydrogenase [sarkosindehydrogenasa]

topical
1
Terms

sarkosindehydrogenáza

 

Monomethylglycine Dehydrogenase
Sarcosine N-Demethylase

Persistent link   https://www.medvik.cz/link/D050892
Definition

A LIVER mitochondrial matrix flavoenzyme that catalyzes the oxidation of SARCOSINE to GLYCINE and FORMALDEHYDE. Mutation in the enzyme causes sarcosinemia, a rare autosomal metabolic defect characterized by elevated levels of SARCOSINE in BLOOD and URINE.

DUI
D050892 MeSH Browser
CUI
M0078933
History note
2006(1976); use OXIDOREDUCTASES, N-DEMETHYLATING, & SARCOSINE 1976-1979
Public note
2006; SARCOSINE DEHYDROGENASE was indexed under OXIDOREDUCTASES, N-DEMETHYLATING 1976-2004, & under SARCOSINE 1976-1982

SARDH protein, human Chemical MeSH Browser

Sardh protein, mouse Chemical MeSH Browser

Sardh protein, rat Chemical MeSH Browser