Steatocystoma Multiplex [steatocystoma multiplex]

topical
2
Terms

mnohočetný steatocystom
steatocystom mnohočetný

 

Multiple Sebaceous Cysts
Multiplex Steatocystoma
Sebaceous Cysts, Multiple

Persistent link   https://www.medvik.cz/link/D062685
Definition

A disorder characterized by multiple, wide spread cutaneous cysts that often become inflamed and rupture. It is caused by the same mutations in the gene coding for KRT-17 that are causative mutations for Pachyonychia congenita, Type 2. Natal teeth involvement is sometimes associated with steatocystoma multiplex.

DUI
D062685 MeSH Browser
CUI
M0528908
History note
2013
Public note
2013

C Diseases
C16.131.831 Skin Abnormalities 51
C16.131.831.350 Ectodermal Dysplasia 33
C16.131.831.350.856 Pachyonychia Congenita 3
C16.131.831.350.856.500 Steatocystoma Multiplex 2
C16.320.850.250 Ectodermal Dysplasia 33
C16.320.850.250.856 Pachyonychia Congenita 3
C16.320.850.250.856.500 Steatocystoma Multiplex 2
C17.800 Skin Diseases 2 799
C17.800.529 Nail Diseases 177
C17.800.529.594 Pachyonychia Congenita 3
C17.800.529.594.500 Steatocystoma Multiplex 2
C17.800.804 Skin Abnormalities 51
C17.800.804.350 Ectodermal Dysplasia 33
C17.800.804.350.856 Pachyonychia Congenita 3
C17.800.804.350.856.500 Steatocystoma Multiplex 2
C17.800.827.250 Ectodermal Dysplasia 33
C17.800.827.250.856 Pachyonychia Congenita 3
C17.800.827.250.856.500 Steatocystoma Multiplex 2

Sebocystomatosis Disease MeSH Browser

Steatocystoma multiplex with natal teeth Disease MeSH Browser