5-Aminolevulinate Synthetase [5-aminolevulátsynthetasa]

topical
4
Terms

5-ALA syntetáza
5-aminolevulát syntáza
5-aminolevulát syntetáza
5-aminolevulát synthetasa
5-aminolevulátsyntetáza
syntetáza kyseliny aminolevulové
synthetasa kyseliny aminolevulové

 

5-Aminolevulinate Synthase
Aminolevulinic Acid Synthetase
delta-Aminolevulinate Synthase
delta-Aminolevulinic Acid Synthetase

Persistent link   https://www.medvik.cz/link/D000624
Definition

An enzyme of the transferase class that catalyzes condensation of the succinyl group from succinyl coenzyme A with glycine to form delta-aminolevulinate. It is a pyridoxyal phosphate protein and the reaction occurs in mitochondria as the first step of the heme biosynthetic pathway. The enzyme is a key regulatory enzyme in heme biosynthesis. In liver feedback is inhibited by heme. EC 2.3.1.37.

DUI
D000624 MeSH Browser
CUI
M0000954
CAS
Succinyl-CoA:glycine C-Succinyltransferase (decarboxylating)
Previous indexing
Acyltransferases (1966-1971)
History note
98(72)
Public note
98; see AMINOLEVULINIC ACID SYNTHETASE 1972-97

D Chemicals and Drugs
D08.811 Enzymes 1 547
D08.811.913 Transferases 72
D08.811.913.050 Acyltransferases 169
D08.811.913.050.080 Acetyl-CoA C-Acyltransferase 4
D08.811.913.050.134 Acetyltransferases 54
D08.811.913.050.200 Aminoacyltransferases 4
D08.811.913.050.276 5-Aminolevulinate Synthetase 4
D08.811.913.050.331 ATP Citrate (pro-S)-Lyase 7
D08.811.913.050.350 Carnitine Acyltransferases 1
D08.811.913.050.368 Citrate (si)-Synthase 32
D08.811.913.050.614 2-Isopropylmalate Synthase
D08.811.913.050.618 Malate Synthase 1
D08.811.913.050.668 Serine C-Palmitoyltransferase 5
D08.811.913.050.712 Sphingosine N-Acyltransferase 4
D08.811.913.050.799 Sterol O-Acyltransferase 12
D10 Lipids 2 524