Dentinogenesis Imperfecta [dentinogenesis imperfecta]

topical
15
Terms

dědičný opalescentní dentin
dentinogenesis imperfecta bez osteogenesis imperfecta
dentinogenesis imperfecta, typ II
hereditární opalescentní dentin
opalescentní dentin
opaleskující dentin
osteogenesis imperfecta bez dentinogenesis imperfecta

 

Capdepont Teeth
Dentinogenesis Imperfecta 1
Dentinogenesis Imperfecta without Osteogenesis Imperfecta
Dentinogenesis Imperfecta, Shields Type 2
Dentinogenesis Imperfecta, Shields Type II
Hereditary Opalescent Dentin
Opalescent Dentin
Opalescent Teeth without Osteogenesis Imperfecta

Persistent link   https://www.medvik.cz/link/D003811
Definition

An autosomal dominant disorder of tooth development characterized by opalescent dentin resulting in discoloration of the teeth. The dentin develops poorly with low mineral content while the pulp canal is obliterated.

DUI
D003811 MeSH Browser
CUI
M0005958
History note
65
Public note
65

C Diseases
C07.650.800 Tooth Abnormalities 260
C07.650.800.100 Anodontia 129
C07.650.800.250 Dens in Dente 10
C07.650.800.260 Dentin Dysplasia 3
C07.650.800.270 Dentinogenesis Imperfecta 15
C07.650.800.320 Diastema 46
C07.650.800.370 Fused Teeth 7
C07.650.800.600 Odontodysplasia 3
C07.650.800.850 Tooth, Supernumerary 42
C07.793 Tooth Diseases 335
C07.793.700 Tooth Abnormalities 260
C07.793.700.100 Anodontia 129
C07.793.700.250 Dens in Dente 10
C07.793.700.255 Dental Fissures 18
C07.793.700.260 Dentin Dysplasia 3
C07.793.700.270 Dentinogenesis Imperfecta 15
C07.793.700.320 Diastema 46
C07.793.700.370 Fused Teeth 7
C07.793.700.600 Odontodysplasia 3
C07.793.700.850 Tooth, Supernumerary 42
C16.131.850.800 Tooth Abnormalities 260
C16.131.850.800.100 Anodontia 129
C16.131.850.800.250 Dens in Dente 10
C16.131.850.800.260 Dentin Dysplasia 3
C16.131.850.800.270 Dentinogenesis Imperfecta 15
C16.131.850.800.320 Diastema 46
C16.131.850.800.370 Fused Teeth 7
C16.131.850.800.600 Odontodysplasia 3
C16.131.850.800.850 Tooth, Supernumerary 42

Cortical Defects, Wormian Bones, and Dentinogenesis Imperfecta Disease MeSH Browser

Deafness, Autosomal Dominant 39, with Dentinogenesis Imperfecta 1 Disease MeSH Browser

Dentinogenesis imperfecta, shields type 3 Disease MeSH Browser

Osteogenesis Imperfecta with Opalescent Teeth, Blue Sclerae and Wormian Bones, but Without Fractures Disease MeSH Browser

Osteogenesis imperfecta, type 1A Disease MeSH Browser

Spondylometaphyseal dysplasia with dentinogenesis imperfecta Disease MeSH Browser