Immunoproliferative Small Intestinal Disease [imunoproliferační nemoc tenkého střeva]

topical
3
Terms

alfa HCD
imunoproliferativní nemoc tenkého střeva
IPSID
nemoc z těžkých řetězců alfa
nemoc z těžkých řetězců typ IgA
středomořský lymfom

 

alpha-Chain Disease
Heavy Chain Disease, IgA Type
IPSID
Lymphoma, Mediterranean

Persistent link   https://www.medvik.cz/link/D007161
Definition

A condition that is caused by HYPERPLASIA of LYMPHOCYTES in the small intestine (INTESTINE, SMALL) and the mesenteric LYMPH NODES. These lymphocytes produce an anomalous alpha heavy chain protein. Generally, these IPSID patients have either concurrent LYMPHOMA or develop lymphoma within a few years. The disease was first described in the Mediterranean region and is characterized by malabsorption; WEIGHT LOSS; DIARRHEA; and STEATORRHEA.

DUI
D007161 MeSH Browser
CUI
M0011165
Previous indexing
Heavy Chain Disease (1966-1986); Intestinal Neoplasms (1966-1986); Lymphoma (1966-1986)
History note
87
Public note
87

C Diseases
C04 Neoplasms 12 762
C04.557.386 Lymphoma 1 118
C04.557.386.150 Composite Lymphoma 3
C04.557.386.355 Hodgkin Disease 943
C04.557.386.435 Intraocular Lymphoma 7
C04.557.386.480 Lymphoma, Non-Hodgkin 621
C06.301.371.411 Intestinal Neoplasms 425
C06.301.371.411.184 Cecal Neoplasms 15
C06.301.371.411.307 Colorectal Neoplasms 3 613
C06.301.371.411.445 Duodenal Neoplasms 90
C06.301.371.411.501 Ileal Neoplasms 28
C06.301.371.411.523 Jejunal Neoplasms 27
C06.405.249.411 Intestinal Neoplasms 425
C06.405.249.411.184 Cecal Neoplasms 15
C06.405.249.411.307 Colorectal Neoplasms 3 613
C06.405.249.411.445 Duodenal Neoplasms 90
C06.405.249.411.501 Ileal Neoplasms 28
C06.405.249.411.523 Jejunal Neoplasms 27
C06.405.469 Intestinal Diseases 756
C06.405.469.491 Intestinal Neoplasms 425
C06.405.469.491.184 Cecal Neoplasms 15
C06.405.469.491.307 Colorectal Neoplasms 3 613
C06.405.469.491.445 Duodenal Neoplasms 90
C06.405.469.491.501 Ileal Neoplasms 28
C06.405.469.491.523 Jejunal Neoplasms 27
C15.378.147.780 Paraproteinemias 285
C15.378.147.780.490 Heavy Chain Disease 8
C15.604.515.435 Heavy Chain Disease 8
C20.683.515.250 Castleman Disease 61
C20.683.515.515 Infectious Mononucleosis 191
C20.683.515.517 Leukemia, Hairy Cell 94
C20.683.515.528 Leukemia, Lymphoid 476
C20.683.515.710 Lymphangiomyoma 1
C20.683.515.761 Lymphoma 1 118
C20.683.515.840 Marek Disease 7
C20.683.515.845 Multiple Myeloma 1 775
C20.683.515.880 Plasmacytoma 179
C20.683.515.920 Sezary Syndrome 43
C20.683.515.950 Tumor Lysis Syndrome 38
C20.683.780 Paraproteinemias 285
C20.683.780.490 Heavy Chain Disease 8