Jaundice, Chronic Idiopathic [žloutenka chronická idiopatická]

topical
25
Terms

chronická idiopatická žloutenka
Dubin-Johnsonův syndrom
Dubinův-Johnsonův syndrom
Dubinův-Sprinzův syndrom
hyperbilirubinemie II
hyperbilirubinémie II
Sprinzův-Nelsonův syndrom

 

Dubin-Johnson Syndrome
Hyperbilirubinemia 2
Hyperbilirubinemia II

Persistent link   https://www.medvik.cz/link/D007566
Definition

A benign, autosomally recessive inherited hyperbilirubinemia characterized by the presence of a dark pigment in the centrilobular region of the liver cells. There is a functional defect in biliary excretion of bilirubin, cholephilic dyes, and porphyrins. Affected persons may be asymptomatic or have vague constitutional or gastrointestinal symptoms. The liver may be slightly enlarged, and oral and intravenous cholangiography fails to visualize the biliary tract.

DUI
D007566 MeSH Browser
CUI
M0011823

C Diseases
C16.320.565.300.281 Crigler-Najjar Syndrome 19
C16.320.565.300.528 Gilbert Disease 51
C16.320.565.300.764 Jaundice, Chronic Idiopathic 25
C16.614.451.500 Jaundice, Neonatal 187
C16.614.451.500.250 Jaundice, Chronic Idiopathic 25
C18.452 Metabolic Diseases 1 200
C18.452.648.300.281 Crigler-Najjar Syndrome 19
C18.452.648.300.528 Gilbert Disease 51
C18.452.648.300.764 Jaundice, Chronic Idiopathic 25
C23.550.291 Disease Attributes 1 208
C23.550.291.500 Chronic Disease 5 064
C23.550.291.500.063 Brain Damage, Chronic 253
C23.550.291.500.313 Chronic Periodontitis 57
C23.550.291.500.360 Chronic Urticaria 17
C23.550.291.500.392 Fatigue Syndrome, Chronic 276
C23.550.291.500.423 Granulomatous Disease, Chronic 54
C23.550.291.500.431 Hematoma, Subdural, Chronic 25
C23.550.291.500.477 Hepatitis, Chronic 127
C23.550.291.500.479 Jaundice, Chronic Idiopathic 25
C23.550.291.500.497 Leukemia, Neutrophilic, Chronic 7
C23.550.291.500.500 Multiple Chronic Conditions 9
C23.550.291.500.750 Pancreatitis, Chronic 235
C23.550.291.500.829 Post-Infectious Disorders
C23.550.291.500.906 Renal Insufficiency, Chronic 751
C23.550.291.500.937 Wasting Disease, Chronic 11