Pierre Robin Syndrome [Pierre Robinův syndrom]

topical
20
Terms

sekvence Pierre Robinova

 

Glossoptosis, Micrognathia, and Cleft Palate
Pierre Robin Sequence
Pierre Robin's Sequence
Pierre-Robin Syndrome
Robin Sequence

Persistent link   https://www.medvik.cz/link/D010855
Definition

Congenital malformation characterized by MICROGNATHIA or RETROGNATHIA; GLOSSOPTOSIS and CLEFT PALATE. The mandibular abnormalities often result in difficulties in sucking and swallowing. The syndrome may be isolated or associated with other syndromes (e.g., ANDERSEN SYNDROME; CAMPOMELIC DYSPLASIA). Developmental mis-expression of SOX9 TRANSCRIPTION FACTOR gene on chromosome 17q and its surrounding region is associated with the syndrome.

Annotation
named for French dentist Pierre Robin: Robin is his surname; note: no hyphen
název po francouzském stomatologovi Pierru Robinovi; bez pomlčky
DUI
D010855 MeSH Browser
CUI
M0016846
History note
65(64)
Public note
65

C Diseases
C05.500 Jaw Diseases 134
C05.500.460 Jaw Abnormalities 171
C05.500.460.185 Cleft Palate 734
C05.500.460.457 Micrognathism 5
C05.500.460.606 Pierre Robin Syndrome 20
C05.500.460.655 Prognathism 18
C05.500.460.827 Retrognathia 8
C05.660.207.540.460 Jaw Abnormalities 171
C05.660.207.540.460.185 Cleft Palate 734
C05.660.207.540.460.457 Micrognathism 5
C05.660.207.540.460.606 Pierre Robin Syndrome 20
C05.660.207.540.460.655 Prognathism 18
C05.660.207.540.460.827 Retrognathia 8
C07.320 Jaw Diseases 134
C07.320.440 Jaw Abnormalities 171
C07.320.440.185 Cleft Palate 734
C07.320.440.457 Micrognathism 5
C07.320.440.606 Pierre Robin Syndrome 20
C07.320.440.655 Prognathism 18
C07.320.440.827 Retrognathia 8
C07.650.500.460 Jaw Abnormalities 171
C07.650.500.460.185 Cleft Palate 734
C07.650.500.460.457 Micrognathism 5
C07.650.500.460.606 Pierre Robin Syndrome 20
C07.650.500.460.655 Prognathism 18
C07.650.500.460.827 Retrognathia 8
C16.131.621.207 Craniofacial Abnormalities 77
C16.131.621.207.540 Maxillofacial Abnormalities 28
C16.131.621.207.540.460 Jaw Abnormalities 171
C16.131.621.207.540.460.185 Cleft Palate 734
C16.131.621.207.540.460.457 Micrognathism 5
C16.131.621.207.540.460.606 Pierre Robin Syndrome 20
C16.131.621.207.540.460.655 Prognathism 18
C16.131.621.207.540.460.827 Retrognathia 8
C16.131.850.500.460 Jaw Abnormalities 171
C16.131.850.500.460.185 Cleft Palate 734
C16.131.850.500.460.457 Micrognathism 5
C16.131.850.500.460.606 Pierre Robin Syndrome 20
C16.131.850.500.460.655 Prognathism 18
C16.131.850.500.460.827 Retrognathia 8

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Robin sequence and oligodactyly Disease MeSH Browser

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