properdin [Properdin]

tematický
22
Termíny

Complement Factor P

Perzistentní odkaz   https://www.medvik.cz/link/D011414
Definice

A 53-kDa protein that is a positive regulator of the alternate pathway of complement activation (COMPLEMENT ACTIVATION PATHWAY, ALTERNATIVE). It stabilizes the ALTERNATIVE PATHWAY C3 CONVERTASE (C3bBb) and protects it from rapid inactivation, thus facilitating the cascade of COMPLEMENT ACTIVATION and the formation of MEMBRANE ATTACK COMPLEX. Individuals with mutation in the PFC gene exhibit properdin deficiency and have a high susceptibility to infections.

DUI
D011414 MeSH Prohlížeč
CUI
M0017748
CAS
Complement factor P

D Chemikálie a léčiva
D12.776 proteiny 2 575
D12.776.124 krevní proteiny 909
D12.776.124.486 imunoproteiny 14
D12.776.124.486.274 komplement 351
D12.776.124.486.274.024 anafylatoxiny 6
D12.776.124.486.274.045 enzymy aktivující komplement 3
D12.776.124.486.274.050 komplement C1 10
D12.776.124.486.274.150 komplement C2 5
D12.776.124.486.274.250 komplement C3 40
D12.776.124.486.274.350 komplement 4 22
D12.776.124.486.274.450 komplement C5 26
D12.776.124.486.274.550 komplement C6
D12.776.124.486.274.650 komplement C7
D12.776.124.486.274.750 komplement C8 1
D12.776.124.486.274.850 komplement C9
D12.776.124.486.274.900 komplement - faktor B 3
D12.776.124.486.274.920 inaktivátory komplementu 21
D12.776.124.486.274.930 membranolytický komplex 4
D12.776.124.486.274.965 properdin 22
D12.776.124.790 sérové globuliny 61
D12.776.124.790.223 beta-globuliny 29
D12.776.124.790.223.100 beta-2-mikroglobulin 86
D12.776.124.790.223.160 beta-thromboglobulin 7
D12.776.124.790.223.200 komplement - faktor H 13
D12.776.124.790.223.338 hemopexin 31
D12.776.124.790.223.580 plazminogen 43
D12.776.124.790.223.624 properdin 22
D12.776.124.790.223.800 globulin vázající pohlavní hormony 82
D12.776.124.790.223.839 transferin 259
D12.776.377 globuliny 68
D12.776.377.715 sérové globuliny 61
D12.776.377.715.182 beta-globuliny 29
D12.776.377.715.182.100 beta-2-mikroglobulin 86
D12.776.377.715.182.160 beta-thromboglobulin 7
D12.776.377.715.182.200 komplement - faktor H 13
D12.776.377.715.182.338 hemopexin 31
D12.776.377.715.182.580 plazminogen 43
D12.776.377.715.182.624 properdin 22
D12.776.377.715.182.800 globulin vázající pohlavní hormony 82
D12.776.377.715.182.839 transferin 259