Laron Syndrome [Laronův syndrom]

topical
1
Terms

Laronův nanismus
syndrom necitlivosti na růstový hormon

 

Growth Hormone Insensitivity Syndrome
Growth Hormone Receptor Defect
Growth Hormone Receptor Deficiency
Laron Dwarfism
Laron Type Dwarfism I
Pituitary Dwarfism II
Primary GH Resistance
Primary Growth Hormone Resistance
Severe GH Insensitivity

Persistent link   https://www.medvik.cz/link/D046150
Definition

An autosomal recessive disorder characterized by short stature, defective GROWTH HORMONE RECEPTOR, and failure to generate INSULIN-LIKE GROWTH FACTOR I by GROWTH HORMONE. Laron syndrome is not a form of primary pituitary dwarfism (GROWTH HORMONE DEFICIENCY DWARFISM) but the result of mutation of the human GHR gene on chromosome 5.

DUI
D046150 MeSH Browser
CUI
M0452907
Previous indexing
Dwarfism (1976-2004); Growth Hormone (1976-2004); Receptors, Cell Surface (1976-2004); Receptors, Somatotropin (1991-2004)
History note
2005
Public note
2005

C Diseases
C05.116 Bone Diseases 796
C05.116.099.343 Dwarfism 99
C05.116.099.343.110 Achondroplasia 71
C05.116.099.343.250 Cockayne Syndrome 4
C05.116.099.343.347 Congenital Hypothyroidism 151
C05.116.099.343.445 Dwarfism, Pituitary 50
C05.116.099.343.679 Laron Syndrome 1
C05.116.099.343.796 Mulibrey Nanism 1
C05.116.099.343.957 Weill-Marchesani Syndrome 1
C16.320.240 Dwarfism 99
C16.320.240.500 Achondroplasia 71
C16.320.240.562 Cockayne Syndrome 4
C16.320.240.625 Congenital Hypothyroidism 151
C16.320.240.750 Laron Syndrome 1
C16.320.240.875 Mulibrey Nanism 1
C16.320.240.937 Silver-Russell Syndrome 3
C19.297 Dwarfism 99
C19.297.312 Dwarfism, Pituitary 50
C19.297.656 Laron Syndrome 1

Laron syndrome type 2 Disease MeSH Browser