Fibrillins [fibriliny]

topical
Terms

fibrilin

 

Fibrillin

Definition

A family of extracellular matrix glycoproteins that is structurally similar to LATENT TGF-BETA BINDING PROTEINS, but contain additional TGF-beta binding domains, in addition to unique domains at their N and C-terminals. Fibrillins assemble into 10-12 nm MICROFIBRILS that function in a variety of cell interactions with the EXTRACELLULAR MATRIX and developmental processes such as ELASTIC TISSUE maintenance and assembly, and the targeting of growth factors to the extracellular matrix.

DUI
D000071837 MeSH Browser
CUI
M000615581
History note
2017; use FIBRILLIN 1985-2016
Public note
2017; see FIBRILLIN 1985-2016

D Chemicals and Drugs
D09.400.430 Glycoproteins 638
D09.400.430.250 Activins 3
D09.400.430.500 ADAM Proteins 14
D09.400.430.563 alpha 1-Antichymotrypsin 1
D09.400.430.594 alpha 1-Antitrypsin 80
D09.400.430.610 alpha-2-Antiplasmin 6
D09.400.430.618 alpha-2-HS-Glycoprotein 8
D09.400.430.625 Anti-Mullerian Hormone 48
D09.400.430.657 Asialoglycoproteins 5
D09.400.430.673 Avidin 14
D09.400.430.681 B-Cell Activating Factor 37
D09.400.430.685 4-1BB Ligand 1
D09.400.430.687 beta 2-Glycoprotein I 14
D09.400.430.688 CD27 Ligand
D09.400.430.750 Clusterin 25
D09.400.430.775 Colony-Stimulating Factors 19
D09.400.430.800 Fibrillins
D09.400.430.800.500 Fibrillin-1 1
D09.400.430.800.750 Fibrillin-2
D09.400.430.825 Glycated Proteins 1
D09.400.430.850 Glycodelin 1
D09.400.430.860 Hemopexin 31
D09.400.430.870 HSP47 Heat-Shock Proteins 4
D09.400.430.883 Inhibins 33
D09.400.430.887 Lactoferrin 32
D09.400.430.890 Membrane Glycoproteins 201
D09.400.430.900 Mucoproteins 77
D09.400.430.910 Myelin P0 Protein 8
D09.400.430.912 Osteonectin 11
D09.400.430.915 Protein C 111
D09.400.430.920 Protein S 36
D09.400.430.930 Proteoglycans 146
D09.400.430.940 Serum Amyloid P-Component 32
D09.400.430.950 Sialoglycoproteins 19
D09.400.430.952 Thyroglobulin 155
D09.400.430.955 Thyroxine-Binding Proteins 38
D09.400.430.960 Transcortin 8
D09.400.430.965 Tumor Necrosis Factor-alpha 1 316
D09.400.430.982 Vitronectin 7
D12.776 Proteins 2 579
D12.776.395 Glycoproteins 638
D12.776.395.022 Activins 3
D12.776.395.033 ADAM Proteins 14
D12.776.395.045 alpha 1-Antichymotrypsin 1
D12.776.395.068 alpha 1-Antitrypsin 80
D12.776.395.080 alpha-2-Antiplasmin 6
D12.776.395.086 alpha-2-HS-Glycoprotein 8
D12.776.395.089 Anti-Mullerian Hormone 48
D12.776.395.092 CD27 Ligand
D12.776.395.140 Asialoglycoproteins 5
D12.776.395.175 Avidin 14
D12.776.395.191 B-Cell Activating Factor 37
D12.776.395.192 4-1BB Ligand 1
D12.776.395.195 beta 2-Glycoprotein I 14
D12.776.395.207 Clusterin 25
D12.776.395.240 Colony-Stimulating Factors 19
D12.776.395.341 Fibrillins
D12.776.395.341.500 Fibrillin-1 1
D12.776.395.341.750 Fibrillin-2
D12.776.395.351 Glycated Proteins 1
D12.776.395.361 Glycodelin 1
D12.776.395.401 Hemopexin 31
D12.776.395.420 HSP47 Heat-Shock Proteins 4
D12.776.395.439 Inhibins 33
D12.776.395.507 Lactoferrin 32
D12.776.395.550 Membrane Glycoproteins 201
D12.776.395.560 Mucoproteins 77
D12.776.395.570 Myelin P0 Protein 8
D12.776.395.600 Osteonectin 11
D12.776.395.635 Protein C 111
D12.776.395.642 Protein S 36
D12.776.395.650 Proteoglycans 146
D12.776.395.690 Serum Amyloid P-Component 32
D12.776.395.700 Sialoglycoproteins 19
D12.776.395.768 Thyroglobulin 155
D12.776.395.832 Thyroxine-Binding Proteins 38
D12.776.395.901 Transcortin 8
D12.776.395.930 Tumor Necrosis Factor-alpha 1 316
D12.776.395.970 Vitronectin 7
D12.776.860 Scleroproteins 5
D12.776.860.300.085 ADAMTS Proteins
D12.776.860.300.140 Aggrecans 7
D12.776.860.300.250 Collagen 1 257
D12.776.860.300.350 Elastin 136
D12.776.860.300.400 Fibrillins
D12.776.860.300.400.500 Fibrillin-1 1
D12.776.860.300.400.750 Fibrillin-2
D12.776.860.300.450 Fibronectins 112
D12.776.860.300.562 Integrin-Binding Sialoprotein 1
D12.776.860.300.675 Laminin 51
D12.776.860.300.700 Matrilin Proteins 1
D12.776.860.300.716 Matrix Gla Protein 1
D12.776.860.300.731 Netrins 1
D12.776.860.300.762 Osteopontin 31
D12.776.860.300.773 Periostin 1
D12.776.860.300.779 Peroxidasin
D12.776.860.300.784 Reelin Protein
D12.776.860.300.850 Tenascin 21
D12.776.860.300.885 Versicans 6
D12.776.860.300.920 Vitronectin 7

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