Amyotrophic Lateral Sclerosis [amyotrofická laterální skleróza]

topical
231
Terms

ALS
amyotrofická laterální skleróza s demencí
amyotrofická laterální skleróza, guamská forma
amyotrofická laterální skleróza/parkinsonizmus demence komplex
Charcotova choroba
Charcotova nemoc
guamská nemoc
Lou Gehrigova nemoc

 

ALS - Amyotrophic Lateral Sclerosis
Amyotrophic Lateral Sclerosis With Dementia
Amyotrophic Lateral Sclerosis-Parkinsonism-Dementia Complex 1
Amyotrophic Lateral Sclerosis, Guam Form
Amyotrophic Lateral Sclerosis, Parkinsonism-Dementia Complex of Guam
Charcot Disease
Dementia With Amyotrophic Lateral Sclerosis
Gehrig's Disease
Guam Disease
Guam Form of Amyotrophic Lateral Sclerosis
Lou Gehrig Disease
Lou Gehrig's Disease
Lou-Gehrigs Disease
Motor Neuron Disease, Amyotrophic Lateral Sclerosis

Persistent link   https://www.medvik.cz/link/D000690
Definition

A degenerative disorder affecting upper MOTOR NEURONS in the brain and lower motor neurons in the brain stem and SPINAL CORD. Disease onset is usually after the age of 50 and the process is usually fatal within 3 to 6 years. Clinical manifestations include progressive weakness, atrophy, FASCICULATION, hyperreflexia, DYSARTHRIA, dysphagia, and eventual paralysis of respiratory function. Pathologic features include the replacement of motor neurons with fibrous ASTROCYTES and atrophy of anterior SPINAL NERVE ROOTS and corticospinal tracts. (From Adams et al., Principles of Neurology, 6th ed, pp1089-94)

DUI
D000690 MeSH Browser
CUI
M0001056

C Diseases
C10.228.854 Spinal Cord Diseases 310
C10.228.854.468 Muscular Atrophy, Spinal 129
C10.228.854.525 Myelitis 50
C10.228.854.583 Pneumorrhachis 1
C10.228.854.761 Spinal Cord Compression 226
C10.228.854.763 Spinal Cord Injuries 818
C10.228.854.765 Spinal Cord Neoplasms 112
C10.228.854.790 Stiff-Person Syndrome 14
C10.228.854.833 Syringomyelia 56
C10.228.854.889 Tabes Dorsalis 19
C10.574.562 Motor Neuron Disease 63
C10.574.562.300 Bulbar Palsy, Progressive 13
C10.574.562.500 Muscular Atrophy, Spinal 129
C10.668.467 Motor Neuron Disease 63
C10.668.467.300 Bulbar Palsy, Progressive 13
C10.668.467.500 Muscular Atrophy, Spinal 129
C18.452 Metabolic Diseases 1 196
C18.452.845.800 TDP-43 Proteinopathies 13
C18.452.845.800.050 Amyotrophic Lateral Sclerosis 231

Amyotrophic Lateral Sclerosis 10 Disease MeSH Browser

Amyotrophic Lateral Sclerosis 11 Disease MeSH Browser

Amyotrophic Lateral Sclerosis 2, Juvenile Disease MeSH Browser

Amyotrophic Lateral Sclerosis 3 Disease MeSH Browser

Amyotrophic Lateral Sclerosis 4, Juvenile Disease MeSH Browser

Amyotrophic Lateral Sclerosis 5 Disease MeSH Browser

Amyotrophic Lateral Sclerosis 6, Autosomal Recessive Disease MeSH Browser

Amyotrophic Lateral Sclerosis 7 Disease MeSH Browser

Amyotrophic Lateral Sclerosis 8 Disease MeSH Browser

Amyotrophic Lateral Sclerosis 9 Disease MeSH Browser

Amyotrophic Lateral Sclerosis With Polyglucosan Bodies Disease MeSH Browser

Amyotrophic Lateral Sclerosis, Autosomal Recessive Disease MeSH Browser

Amyotrophic Lateral Sclerosis, Juvenile, with Dementia Disease MeSH Browser

Amyotrophic lateral sclerosis 1 Disease MeSH Browser

Amyotrophic lateral sclerosis, type 6 Disease MeSH Browser

Frontotemporal Dementia With Motor Neuron Disease Disease MeSH Browser