Skupina autoimunitních onemocnění charakterizovaných generalizovaným postižením vaziva a pojiva, postiženy jsou i další orgány (zejm. kůže, plíce, ledviny, srdce a cévy). Patří sem zejména: systémový lupus erythematodes (SLE), Sharpův syndrom, sklerodermie, polymyositida/dermatomyositida, Sjögrenův syndrom, CREST syndrom. (cit. Wikiskripta 2017 http://www.wikiskripta.eu/)

Historically, a heterogeneous group of acute and chronic diseases, including rheumatoid arthritis, systemic lupus erythematosus, progressive systemic sclerosis, dermatomyositis, etc. This classification was based on the notion that collagen was equivalent to connective tissue, but with the present recognition of the different types of collagen and the aggregates derived from them as distinct entities, the term collagen diseases now pertains exclusively to those inherited conditions in which the primary defect is at the gene level and affects collagen biosynthesis, post-translational modification, or extracellular processing directly. (From Cecil Textbook of Medicine, 19th ed, p1494)

Anotace

general or unspecified; prefer specifics

obecné, dej přednost přesnějšímu deskriptoru

DUI

D003095 MeSH Prohlížeč

CUI

M0004792