Dermatomyositis [dermatomyozitida]

topical
239
Terms

dermatomyozitida u dospělých
dermatopolymyozitida
dětská dermatomyozitida
juvenilní dermatomyozitida
polymyozitida - dermatomyozitida

 

Dermatomyositis, Adult Type
Dermatomyositis, Childhood Type
Dermatopolymyositis
Juvenile Dermatomyositis
Juvenile Myositis
Polymyositis-Dermatomyositis

Persistent link   https://www.medvik.cz/link/D003882
Definition

A subacute or chronic inflammatory disease of muscle and skin, marked by proximal muscle weakness and a characteristic skin rash. The illness occurs with approximately equal frequency in children and adults. The skin lesions usually take the form of a purplish rash (or less often an exfoliative dermatitis) involving the nose, cheeks, forehead, upper trunk, and arms. The disease is associated with a complement mediated intramuscular microangiopathy, leading to loss of capillaries, muscle ischemia, muscle-fiber necrosis, and perifascicular atrophy. The childhood form of this disease tends to evolve into a systemic vasculitis. Dermatomyositis may occur in association with malignant neoplasms. (From Adams et al., Principles of Neurology, 6th ed, pp1405-6)

Annotation
coordinate with PARANEOPLASTIC SYNDROMES if pertinent
DUI
D003882 MeSH Browser
CUI
M0006061

C Diseases
C05.651.594 Myositis 250
C05.651.594.819 Polymyositis 149
C05.651.594.819.500 Dermatomyositis 239
C10.668.491 Muscular Diseases 552
C10.668.491.562 Myositis 250
C10.668.491.562.575 Polymyositis 149
C10.668.491.562.575.500 Dermatomyositis 239
C17.300.116 Anetoderma 5
C17.300.182 Cartilage Diseases 140
C17.300.185 Cellulitis 132
C17.300.200 Collagen Diseases 183
C17.300.230 Cutis Laxa 10
C17.300.250 Dermatomyositis 239
C17.300.428 Homocystinuria 107
C17.300.451 Lipedema 20
C17.300.500 Marfan Syndrome 105
C17.300.550 Mucinoses 17
C17.300.690 Noonan Syndrome 51
C17.300.705 Osteopoikilosis 6
C17.300.710 Panniculitis 42
C17.300.715 Penile Induration 48
C17.300.775 Rheumatic Diseases 2 175
C17.300.799 Scleroderma, Systemic 482
C17.800 Skin Diseases 2 796
C17.800.030 Acneiform Eruptions 33
C17.800.090 Breast Diseases 349
C17.800.113 Calcinosis Cutis
C17.800.135 Cutaneous Fistula 25
C17.800.174 Dermatitis 332
C17.800.185 Dermatomyositis 239
C17.800.229 Erythema 199
C17.800.257 Exanthema 303
C17.800.271 Facial Dermatoses 130
C17.800.321 Foot Diseases 209
C17.800.329 Hair Diseases 174
C17.800.338 Hand Dermatoses 54
C17.800.417 Keratoacanthoma 24
C17.800.428 Keratosis 133
C17.800.446 Leg Dermatoses 24
C17.800.463 Lipomatosis 36
C17.800.529 Nail Diseases 177
C17.800.566 Panniculitis 42
C17.800.621 Pigmentation Disorders 132
C17.800.674 Prurigo 18
C17.800.685 Pruritus 266
C17.800.695 Pyoderma 68
C17.800.716 Rosacea 140
C17.800.738 Scalp Dermatoses 37
C17.800.784 Scleroderma, Systemic 482
C17.800.804 Skin Abnormalities 51
C17.800.882 Skin Neoplasms 1 647
C17.800.893 Skin Ulcer 139