Muscular Atrophy, Spinal [spinální svalová atrofie]
- Terms
-
amyotrofie
bulbospinální neuronopatie
distální spinální svalová atrofie
hereditární motorická neuronopatie
míšní svalová atrofie
myelopatická svalová atrofie
okulofaryngeální spinální svalová atrofie
progresivní proximální myelopatická svalová atrofie
progresivní svalová atrofie
skapuloperoneální forma spinální svalové atrofie
spinální muskulární atrofie
svalová atrofie páteře
-
Adult Spinal Muscular Atrophy
Adult-Onset Spinal Muscular Atrophy
Amyotrophy, Neurogenic Scapuloperoneal, New England Type
Bulbospinal Neuronopathy
Distal Spinal Muscular Atrophy
Hereditary Motor Neuronopathy
Muscular Atrophy, Adult Spinal
Myelopathic Muscular Atrophy
Myelopathic Muscular Atrophy, Progressive
Oculopharyngeal Spinal Muscular Atrophy
Progressive Muscular Atrophy
Progressive Myelopathic Muscular Atrophy
Progressive Proximal Myelopathic Muscular Atrophy
Proximal Myelopathic Muscular Atrophy, Progressive
Scapuloperoneal Form of Spinal Muscular Atrophy
Scapuloperoneal Spinal Muscular Atrophy
Spinal Amyotrophy
Spinal Muscular Atrophy
Spinal Muscular Atrophy, Distal
Spinal Muscular Atrophy, Oculopharyngeal
Spinal Muscular Atrophy, Scapuloperoneal
Spinal Muscular Atrophy, Scapuloperoneal Form
A group of disorders marked by progressive degeneration of motor neurons in the spinal cord resulting in weakness and muscular atrophy, usually without evidence of injury to the corticospinal tracts. Diseases in this category include Werdnig-Hoffmann disease and later onset SPINAL MUSCULAR ATROPHIES OF CHILDHOOD, most of which are hereditary. (Adams et al., Principles of Neurology, 6th ed, p1089)
- Annotation
- MUSCULAR ATROPHY, SPINAL, INFANTILE see SPINAL MUSCULAR ATROPHIES OF CHILDHOOD is also available
- DUI
- D009134 MeSH Browser
- CUI
- M0014250
- Previous indexing
- Muscular Atrophy (1966-1987); Spinal Cord Diseases (1966-1987)
- History note
- 1988
- Public note
- 1988
Allowable subheadings
- BL
- blood
- CF
- cerebrospinal fluid
- CI
- chemically induced
- CL
- classification 9
- CO
- complications 4
- CN
- congenital 2
- DI
- diagnosis 35
- DG
- diagnostic imaging
- DH
- diet therapy 1
- DT
- drug therapy 17
- EC
- economics 4
- EM
- embryology
- EN
- enzymology
- EP
- epidemiology 6
- EH
- ethnology
- ET
- etiology 11
- GE
- genetics 36
- HI
- history
- IM
- immunology 1
- ME
- metabolism
- MI
- microbiology
- MO
- mortality
- NU
- nursing 3
- PS
- parasitology
- PA
- pathology 9
- PP
- physiopathology 11
- PC
- prevention & control 1
- PX
- psychology 2
- RT
- radiotherapy
- RH
- rehabilitation 6
- SU
- surgery 5
- TH
- therapy 30
- UR
- urine
- VE
- veterinary
- VI
- virology
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Neuronopathy, Distal Hereditary Motor, Type IIB Disease MeSH Browser
Neuronopathy, Distal Hereditary Motor, Type V Disease MeSH Browser
Neuronopathy, Distal Hereditary Motor, Type Viib Disease MeSH Browser
Neuropathy, Distal Hereditary Motor, Type IIA Disease MeSH Browser
Neuropathy, Distal Hereditary Motor, Type VIIA Disease MeSH Browser
Scapuloperoneal Syndrome, Neurogenic, Kaeser Type Disease MeSH Browser
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Spinal Muscular Atrophy, Facioscapulohumeral Type Disease MeSH Browser
Spinal Muscular Atrophy, Late-Onset, Finkel Type Disease MeSH Browser
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Spinal muscular atrophy with respiratory distress 1 Disease MeSH Browser
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