Polyendocrinopathies, Autoimmune [autoimunitní polyglandulární syndromy]

topical
110
Terms

APECED
APS
APS-1
autoimunitní polyendokrinopatie s kandidózou a ektodermální dystrofií
autoimunitní polyglandulární postižení
autoimunitní polyglandulární syndrom
autoimunitní polyglandulární syndrom typu 1
autoimunitní polyglandulární syndrom typu 2
autoimunitní polyglandulární syndrom typu 3
autoimunitní polyglandulární syndrom typu III
autoimunitní syndrom polyglandulární typ I
autoimunitní syndrom polyglandulární typ II
Blizzardův syndrom
PGAD
polyendokrinopatie autoimunitní
polyglandulární autoimunitní endokrinní syndrom
polyglandulární syndrom
Schmidtův syndrom (endokrinní)
Whitakerův syndrom

 

AIRE Deficiency
APECED
APS Type 1
Autoimmune Polyendocrine Syndrome, Type 2
Autoimmune Polyendocrine Syndrome, Type II
Autoimmune Polyendocrinopathy Syndrome Type 1
Autoimmune Polyendocrinopathy with Candidiasis and Ectodermal Dystrophy
Autoimmune Polyendocrinopathy-Candidiasis-Ectodermal Dystrophy
Autoimmune Polyendocrinopathy-Candidiasis-Ectodermal-Dystrophy
Autoimmune Polyglandular Syndrome Type I
Autoimmune Polyglandular Syndrome Type II
Autoimmune Polyglandular Syndrome Type III
Autoimmune Polyglandular Syndrome, Type 1
Autoimmune Polyglandular Syndrome, Type 3
Autoimmune Polyglandular Syndrome, Type I
Autoimmune Syndrome Type I, Polyglandular
Autoimmune Syndrome Type II, Polyglandular
Autoimmune Syndrome Type III, Polyglandular
Diabetes Mellitus, Addison Disease, Myxedema
Diabetes Mellitus, Addison's Disease, Myxedema
Multiple Endocrine Deficiency Syndrome, Type 2
Polyendocrine Autoimmune Syndrome, Type II
Polyendocrinopathy-Candidiasis-Ectodermal-Dystrophy, Autoimmune
Polyglandular Autoimmune Syndrome, Type 1
Polyglandular Autoimmune Syndrome, Type 2
Polyglandular Autoimmune Syndrome, Type 3
Polyglandular Autoimmune Syndrome, Type I
Polyglandular Deficiency Syndrome, Type 2
Polyglandular Type I Autoimmune Syndrome
Polyglandular Type II Autoimmune Syndrome
Polyglandular Type III Autoimmune Syndrome
Schmidt Syndrome
Schmidt's Syndrome

Persistent link   https://www.medvik.cz/link/D016884
Definition

Autoimmune diseases affecting multiple endocrine organs. Type I is characterized by childhood onset and chronic mucocutaneous candidiasis (CANDIDIASIS, CHRONIC MUCOCUTANEOUS), while type II exhibits any combination of adrenal insufficiency (ADDISON'S DISEASE), lymphocytic thyroiditis (THYROIDITIS, AUTOIMMUNE;), HYPOPARATHYROIDISM; and gonadal failure. In both types organ-specific ANTIBODIES against a variety of ENDOCRINE GLANDS have been detected. The type II syndrome differs from type I in that it is associated with HLA-A1 and B8 haplotypes, onset is usually in adulthood, and candidiasis is not present.

Annotation
do not coordinate with specific endocrine disease term or CANDIDIASIS unless particularly discussed
DUI
D016884 MeSH Browser
CUI
M0025689
Previous indexing
Autoimmune Diseases (1968-1991); Endocrine Diseases (1978-1991)
History note
1992
Public note
1992

C Diseases
C19.246 Diabetes Mellitus 9 524
C19.297 Dwarfism 97
C19.874 Thyroid Diseases 1 302
C20.111 Autoimmune Diseases 1 932
C20.111.163 Addison Disease 128
C20.111.198 Arthritis, Juvenile 474
C20.111.199 Arthritis, Rheumatoid 3 114
C20.111.327 Diabetes Mellitus, Type 1 3 001
C20.111.555 Graves Disease 255
C20.111.730 Pemphigoid, Bullous 87
C20.111.736 Pemphigus 207