Anti-Glomerular Basement Membrane Disease [antirenální glomerulonefritida]

topical
47
Terms

anti-GBM nefritida
anti-GBM nemoc
autoimunitní glomerulonefritida
Goodpastureova choroba
Goodpastureova nemoc
Goodpastureův syndrom

 

Anti-GBM Disease
Goodpasture Syndrome
Goodpasture's Syndrome
Lung Purpura with Nephritis

Persistent link   https://www.medvik.cz/link/D019867
Definition

An autoimmune disease of the KIDNEY and the LUNG. It is characterized by the presence of circulating autoantibodies targeting the epitopes in the non-collagenous domains of COLLAGEN TYPE IV in the basement membranes of kidney glomeruli (KIDNEY GLOMERULUS) and lung alveoli (PULMONARY ALVEOLI), and the subsequent destruction of these basement membranes. Clinical features include pulmonary alveolar hemorrhage and glomerulonephritis.

DUI
D019867 MeSH Browser
CUI
M0029493
History note
1998
Public note
1998; for GOODPASTURE SYNDROME see GOODPASTURE SYNDROME 1965-2006

C Diseases
C08.381 Lung Diseases 2 196
C08.381.483.581 Pneumoconiosis 406
C08.381.483.652 Pulmonary Fibrosis 489
C08.381.483.675 Radiation Pneumonitis 29
C08.381.483.725 Sarcoidosis, Pulmonary 167
C12.050.351.968 Urologic Diseases 836
C12.050.351.968.419 Kidney Diseases 3 067
C12.050.351.968.419.570 Nephritis 159
C12.050.351.968.419.570.363 Glomerulonephritis 662
C12.050.351.968.419.570.363.304 Anti-Glomerular Basement Membrane Disease 47
C12.050.351.968.419.570.363.608 Glomerulonephritis, IGA 210
C12.050.351.968.419.570.363.615 Glomerulonephritis, Membranoproliferative 28
C12.050.351.968.419.570.363.625 Glomerulonephritis, Membranous 79
C12.050.351.968.419.570.363.640 Glomerulosclerosis, Focal Segmental 99
C12.050.351.968.419.570.363.680 Lupus Nephritis 162
C12.200.777 Urologic Diseases 836
C12.200.777.419 Kidney Diseases 3 067
C12.200.777.419.570 Nephritis 159
C12.200.777.419.570.363 Glomerulonephritis 662
C12.200.777.419.570.363.304 Anti-Glomerular Basement Membrane Disease 47
C12.200.777.419.570.363.608 Glomerulonephritis, IGA 210
C12.200.777.419.570.363.615 Glomerulonephritis, Membranoproliferative 28
C12.200.777.419.570.363.625 Glomerulonephritis, Membranous 79
C12.200.777.419.570.363.660 Glomerulosclerosis, Focal Segmental 99
C12.200.777.419.570.363.680 Lupus Nephritis 162
C12.950.419 Kidney Diseases 3 067
C12.950.419.570 Nephritis 159
C12.950.419.570.363 Glomerulonephritis 662
C12.950.419.570.363.608 Glomerulonephritis, IGA 210
C12.950.419.570.363.625 Glomerulonephritis, Membranous 79
C12.950.419.570.363.640 Glomerulosclerosis, Focal Segmental 99
C12.950.419.570.363.680 Lupus Nephritis 162
C20.111 Autoimmune Diseases 1 940
C20.111.163 Addison Disease 129
C20.111.198 Arthritis, Juvenile 476
C20.111.199 Arthritis, Rheumatoid 3 132
C20.111.327 Diabetes Mellitus, Type 1 3 017
C20.111.555 Graves Disease 255
C20.111.730 Pemphigoid, Bullous 87
C20.111.736 Pemphigus 209