Hexosaminidase B [hexosaminidasa B]

topical
1
Terms

Hex B
hexosaminidáza B
hexozaminidáza B

 

Hex B

Persistent link   https://www.medvik.cz/link/D054819
Definition

A mammalian beta-hexosaminidase isoform that is comprized of hexosaminidase beta subunits. Deficiency of hexosaminidase B due to mutations in the gene encoding the hexosaminidase beta subunit is a case of SANDHOFF DISEASE.

DUI
D054819 MeSH Browser
CUI
M0002424
Previous indexing
beta-N-Acetylhexosaminidases (1987-2007)
History note
2008; use BETA-N-ACETYLHEXOSAMINIDASES 1987-2007
Public note
2008; see BETA-N-ACETYLHEXOSAMINIDASE 1987-2007