Linear IgA Bullous Dermatosis [lineární IgA bulózní dermatóza]

topical
15
Terms

chronická bulózní dermatóza dětí
LABD
léky indukovaná lineární IgA bulózní dermatóza
léky indukovaná lineární IgA dermatóza
lineární IgA dermatóza
lineární IgA IgG bulózní dermatóza
lineární IgA IgG dermatóza

 

Chronic Bullous Disease of Childhood
Drug-induced Linear IgA Bullous Dermatosis
Drug-induced Linear IgA Dermatosis
Linear IgA Dermatosis
Linear IgA IgG Bullous Dermatosis
Linear IgA IgG Dermatosis

Persistent link   https://www.medvik.cz/link/D062027
Definition

Autoimmune disease characterized by subepidermal blisters and linear deposition of autoantibodies at the dermoepidermal junction. The accumulated autoantibodies are of IMMUNOGLOBULIN A and occasionally IMMUNOGLOBULIN G classes against epidermal BASEMENT MEMBRANE proteins. The dermatosis is sometimes associated with malignancies and use of certain drugs (e.g., VANCOMYCIN).

DUI
D062027 MeSH Browser
CUI
M0560975
Previous indexing
Autoimmune Diseases (1980-2012); Skin Diseases (1980-2012)
History note
2013
Public note
2013

C Diseases
C17.800 Skin Diseases 2 796
C17.800.865.070 Acantholysis 10
C17.800.865.187 Blister 58
C17.800.865.360 Dermatitis Herpetiformis 87
C17.800.865.385 Eczema, Dyshidrotic 8
C17.800.865.410 Epidermolysis Bullosa 108
C17.800.865.475 Erythema Multiforme 34
C17.800.865.575 Hydroa Vacciniforme 8
C17.800.865.690 Pemphigoid, Bullous 87
C17.800.865.700 Pemphigoid Gestationis 27
C17.800.865.716 Pemphigus 207
C17.800.865.858 Pemphigus, Benign Familial 11
C20.111 Autoimmune Diseases 1 929
C20.111.163 Addison Disease 128
C20.111.198 Arthritis, Juvenile 472
C20.111.199 Arthritis, Rheumatoid 3 104
C20.111.327 Diabetes Mellitus, Type 1 2 998
C20.111.555 Graves Disease 255
C20.111.730 Pemphigoid, Bullous 87
C20.111.736 Pemphigus 207