Anemia, Sickle Cell [srpkovitá anemie]

topical
45
Terms

anémie srpkovitá
drepanocytóza
falciformní anémie
srpkovitá anémie

 

HbS Disease
Hemoglobin S Disease
Sickle Cell Anemia
Sickle Cell Disease
Sickle Cell Disorders
Sickling Disorder Due to Hemoglobin S

Persistent link   https://www.medvik.cz/link/D000755
Definition

A disease characterized by chronic hemolytic anemia, episodic painful crises, and pathologic involvement of many organs. It is the clinical expression of homozygosity for hemoglobin S.

Annotation
PL 92-294: Natl Sickle Cell Anemia Control Act; sickle cell dis goes here unless specifically HEMOGLOBIN SC DISEASE or HEMOGLOBIN C DISEASE or SICKLE CELL TRAIT or THALASSEMIA; /drug ther: consider also ANTISICKLING AGENTS
DUI
D000755 MeSH Browser
CUI
M0001140

C Diseases
C15.378.050 Anemia 1 244
C15.378.050.141 Anemia, Hemolytic 257
C15.378.050.141.150 Anemia, Hemolytic, Congenital 48
C15.378.050.141.150.095 Anemia, Dyserythropoietic, Congenital 16
C15.378.050.141.150.150 Anemia, Sickle Cell 45
C15.378.050.141.150.150.219 Acute Chest Syndrome 2
C15.378.050.141.150.150.440 Hemoglobin SC Disease 1
C15.378.050.141.150.150.670 Sickle Cell Trait 1
C15.378.050.141.150.150.835 Vaso-Occlusive Crises
C15.378.050.141.150.365 Elliptocytosis, Hereditary 6
C15.378.050.141.150.490 Hemoglobin C Disease 1
C15.378.050.141.150.785 Spherocytosis, Hereditary 43
C15.378.050.141.150.875 Thalassemia 85
C15.378.420 Hemoglobinopathies 68
C15.378.420.155 Anemia, Sickle Cell 45
C15.378.420.155.219 Acute Chest Syndrome 2
C15.378.420.155.440 Hemoglobin SC Disease 1
C15.378.420.155.668 Sickle Cell Trait 1
C15.378.420.155.834 Vaso-Occlusive Crises
C15.378.420.463 Hemoglobin C Disease 1
C15.378.420.826 Thalassemia 85
C16.320.070.150 Anemia, Sickle Cell 45
C16.320.070.150.219 Acute Chest Syndrome 2
C16.320.070.150.440 Hemoglobin SC Disease 1
C16.320.070.150.670 Sickle Cell Trait 1
C16.320.070.150.835 Vaso-Occlusive Crises
C16.320.070.490 Hemoglobin C Disease 1
C16.320.070.785 Spherocytosis, Hereditary 43
C16.320.070.875 Thalassemia 85
C16.320.365 Hemoglobinopathies 68
C16.320.365.155 Anemia, Sickle Cell 45
C16.320.365.155.219 Acute Chest Syndrome 2
C16.320.365.155.440 Hemoglobin SC Disease 1
C16.320.365.155.668 Sickle Cell Trait 1
C16.320.365.155.834 Vaso-Occlusive Crises
C16.320.365.463 Hemoglobin C Disease 1
C16.320.365.826 Thalassemia 85