talasemie [Thalassemia]

tematický
85
Termíny

talasémie
thalasemie
thalassaemia

 

Thalassemias

Perzistentní odkaz   https://www.medvik.cz/link/D013789
Definice

Dědičné krevní onemocnění, při němž je narušena tvorba bílkovinných součástí krevního barviva hemoglobinu. (cit. Velký lékařský slovník online, 2013 http://lekarske.slovniky.cz/ )

A group of hereditary hemolytic anemias in which there is decreased synthesis of one or more hemoglobin polypeptide chains. There are several genetic types with clinical pictures ranging from barely detectable hematologic abnormality to severe and fatal anemia.

Anotace
general or unspecified; prefer specifics
DUI
D013789 MeSH Prohlížeč
CUI
M0021265
Historická pozn.
65; was ANEMIA, ERYTHROBLASTIC 1963-64; ANEMIA, TARGET-CELL was see THALASSEMIA 1965-92
Online pozn.
use THALASSEMIA to search ANEMIA, TARGET-CELL 1966-92
Veřejná pozn.
65; was ANEMIA, ERYTHROBLASTIC 1963-64; ANEMIA, TARGET-CELL was see THALASSEMIA 1965-92

C Nemoci
C15.378 krevní nemoci 973
C15.378.050 anemie 1 244
C15.378.050.141 hemolytické anemie 257
C15.378.050.141.150.150 srpkovitá anemie 45
C15.378.050.141.150.365 dědičná eliptocytóza 6
C15.378.050.141.150.490 hemoglobinopatie s hemoglobinem C 1
C15.378.050.141.150.785 dědičná sférocytóza 43
C15.378.050.141.150.875 talasemie 85
C15.378.050.141.150.875.100 alfa-talasemie 12
C15.378.050.141.150.875.150 beta-talasemie 53
C15.378.050.141.150.875.575 delta-talasemie
C15.378.420 hemoglobinopatie 68
C15.378.420.155 srpkovitá anemie 45
C15.378.420.826 talasemie 85
C15.378.420.826.100 alfa-talasemie 12
C15.378.420.826.150 beta-talasemie 53
C15.378.420.826.200 delta-talasemie
C16.320.070.150 srpkovitá anemie 45
C16.320.070.365 dědičná eliptocytóza 6
C16.320.070.785 dědičná sférocytóza 43
C16.320.070.875 talasemie 85
C16.320.070.875.100 alfa-talasemie 12
C16.320.070.875.150 beta-talasemie 53
C16.320.070.875.575 delta-talasemie
C16.320.365 hemoglobinopatie 68
C16.320.365.155 srpkovitá anemie 45
C16.320.365.826 talasemie 85
C16.320.365.826.100 alfa-talasemie 12
C16.320.365.826.150 beta-talasemie 53
C16.320.365.826.575 delta-talasemie