Congenital Hypothyroidism [kongenitální hypotyreóza]

topical
151
Terms

endemický kretenismus
hypotyreóza kongenitální
kongenitální hypotyreoidismus
kretenismus
myxedém kongenitální
vrozená hypotyreóza

 

Cretinism
Endemic Cretinism
Fetal Iodine Deficiency Disorder
Myxedema, Congenital

Persistent link   https://www.medvik.cz/link/D003409
Definition

A condition in infancy or early childhood due to an in-utero deficiency of THYROID HORMONES that can be caused by genetic or environmental factors, such as thyroid dysgenesis or HYPOTHYROIDISM in infants of mothers treated with THIOURACIL during pregnancy. Endemic cretinism is the result of iodine deficiency. Clinical symptoms include severe MENTAL RETARDATION, impaired skeletal development, short stature, and MYXEDEMA.

DUI
D003409 MeSH Browser
CUI
M0005308
History note
2006 (1966)
Public note
2006; see CRETINISM 1966-2005

C Diseases
C05.116 Bone Diseases 792
C05.116.099.343 Dwarfism 97
C05.116.099.343.110 Achondroplasia 71
C05.116.099.343.250 Cockayne Syndrome 4
C05.116.099.343.347 Congenital Hypothyroidism 151
C05.116.099.343.445 Dwarfism, Pituitary 50
C05.116.099.343.679 Laron Syndrome 1
C05.116.099.343.796 Mulibrey Nanism 1
C05.116.099.343.957 Weill-Marchesani Syndrome 1
C05.116.132.082 Acromegaly 330
C05.116.132.256 Congenital Hypothyroidism 151
C05.116.132.358 Dwarfism, Pituitary 50
C05.116.132.479 Gigantism 14
C05.116.132.684 Osteitis Fibrosa Cystica 9
C16.320.240 Dwarfism 97
C16.320.240.500 Achondroplasia 71
C16.320.240.562 Cockayne Syndrome 4
C16.320.240.625 Congenital Hypothyroidism 151
C16.320.240.750 Laron Syndrome 1
C16.320.240.875 Mulibrey Nanism 1
C16.320.240.937 Silver-Russell Syndrome 3
C19.297 Dwarfism 97
C19.297.312 Dwarfism, Pituitary 50
C19.297.656 Laron Syndrome 1
C19.874 Thyroid Diseases 1 304
C19.874.482 Hypothyroidism 1 049
C19.874.482.281 Congenital Hypothyroidism 151
C19.874.482.638 Myxedema 41

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