Waldenstrom Macroglobulinemia [Waldenströmova makroglobulinemie]

topical
112
Terms

dědičná Waldenstromova makroglobulinemie
dědičná Waldenströmova makroglobulinemie
dědičná Waldenströmova makroglobulinémie
lymfoplazmocytický lymfom
lymfoplazmocytoidní lymfom
primární makroglobulinémie
Waldenströmova makroglobulinémie
Waldenströmova makroglobulinémie dědičná

 

Familial Waldenstrom's Macroglobulinaemia
Lymphoma, Lymphocytic, Plasmacytoid
Lymphoma, Lymphoplasmacytoid
Macroglobulinemia
Primary Macroglobulinemia
Waldenstrom's Macroglobulinaemia
Waldenstrom's Macroglobulinemia

Persistent link   https://www.medvik.cz/link/D008258
Definition

A lymphoproliferative disorder characterized by pleomorphic B-LYMPHOCYTES including PLASMA CELLS, with increased levels of monoclonal serum IMMUNOGLOBULIN M. There is lymphoplasmacytic cells infiltration into bone marrow and often other tissues, also known as lymphoplasmacytic lymphoma. Clinical features include ANEMIA; HEMORRHAGES; and hyperviscosity.

Annotation
in titles & translations use diacritic: Waldenström
DUI
D008258 MeSH Browser
CUI
M0012865
History note
1999 (1963)
Public note
1999; see WALDENSTROM'S MACROGLOBULINEMIA 1992-98, see MACROGLOBULINEMIA 1963-91; for LYMPHOMA, LYMPHOCYTIC, PLASMACYTOID see LYMPHOMA, SMALL CELL 1991-2007

C Diseases
C04 Neoplasms 12 832
C04.557.595.500 Multiple Myeloma 1 790
C04.557.595.600 Plasmacytoma 179
C14.907 Vascular Diseases 1 793
C14.907.454 Hemostatic Disorders 49
C14.907.454.140 Cryoglobulinemia 72
C14.907.454.240 Ehlers-Danlos Syndrome 51
C14.907.454.385 Hemangioma, Cavernous 53
C14.907.454.460 Multiple Myeloma 1 790
C14.907.454.530 Pseudoxanthoma Elasticum 13
C14.907.454.800 Scurvy 28
C14.907.454.810 Shwartzman Phenomenon 10
C15.378.147.780 Paraproteinemias 290
C15.378.147.780.243 Cryoglobulinemia 72
C15.378.147.780.490 Heavy Chain Disease 8
C15.378.147.780.650 Multiple Myeloma 1 790
C15.378.147.780.750 POEMS Syndrome 35
C15.378.147.780.838 Smoldering Multiple Myeloma 12
C15.378.147.780.925 Waldenstrom Macroglobulinemia 112
C15.378.463.515 Hemostatic Disorders 49
C15.378.463.515.140 Cryoglobulinemia 72
C15.378.463.515.240 Ehlers-Danlos Syndrome 51
C15.378.463.515.385 Hemangioma, Cavernous 53
C15.378.463.515.460 Multiple Myeloma 1 790
C15.378.463.515.530 Pseudoxanthoma Elasticum 13
C15.378.463.515.550 Purpura, Hyperglobulinemic 4
C15.378.463.515.580 IgA Vasculitis 76
C15.378.463.515.800 Scurvy 28
C15.378.463.515.810 Shwartzman Phenomenon 10
C15.378.463.515.960 Waldenstrom Macroglobulinemia 112
C15.604.515.032 Agammaglobulinemia 114
C15.604.515.245 Castleman Disease 62
C15.604.515.292 Granuloma 236
C15.604.515.435 Heavy Chain Disease 8
C15.604.515.516 Infectious Mononucleosis 191
C15.604.515.553 Leukemia, Hairy Cell 95
C15.604.515.560 Leukemia, Lymphoid 477
C15.604.515.562 Lymphangiomyoma 1
C15.604.515.569 Lymphoma 1 126
C15.604.515.700 Marek Disease 7
C15.604.515.827 Sarcoidosis 501
C15.604.515.841 Sezary Syndrome 43
C15.604.515.880 Tumor Lysis Syndrome 38
C20.683.780 Paraproteinemias 290
C20.683.780.250 Cryoglobulinemia 72
C20.683.780.490 Heavy Chain Disease 8
C20.683.780.650 Multiple Myeloma 1 790
C20.683.780.750 POEMS Syndrome 35