POEMS Syndrome [POEMS syndrom]

topical
35
Terms

Crow-Fukase syndrom
Crowův-Fukaseův syndrom
osteosklerotický myelom
syndrom Crow-Fukase
syndrom POEMS
Takatsuki syndrom

 

Crow-Fukase Syndrome
Polyneuropathy Organomegaly
Polyneuropathy, Organomegaly, Endocrinopathy, M Protein, and Skin Changes Syndrome
Takatsuki's Syndrome

Persistent link   https://www.medvik.cz/link/D016878
Definition

A multisystemic disorder characterized by a sensorimotor polyneuropathy (POLYNEUROPATHIES), organomegaly, endocrinopathy, monoclonal gammopathy, and pigmentary skin changes. Other clinical features which may be present include EDEMA; CACHEXIA; microangiopathic glomerulopathy; pulmonary hypertension (HYPERTENSION, PULMONARY); cutaneous necrosis; THROMBOCYTOSIS; and POLYCYTHEMIA. This disorder is frequently associated with osteosclerotic myeloma. (From Adams et al., Principles of Neurology, 6th ed, p1335; Rev Med Interne 1997;18(7):553-62)

DUI
D016878 MeSH Browser
CUI
M0025682
History note
1992
Public note
1992

Allowable subheadings

BL
blood 1
CF
cerebrospinal fluid
CI
chemically induced
CL
classification
CO
complications 5
CN
congenital
DI
diagnosis 18
DG
diagnostic imaging 2
DH
diet therapy
DT
drug therapy 5
EC
economics
EM
embryology
EN
enzymology
EP
epidemiology
EH
ethnology
ET
etiology 1
GE
genetics
HI
history
IM
immunology 1
ME
metabolism
MI
microbiology
MO
mortality 1
NU
nursing
PS
parasitology
PA
pathology 6
PP
physiopathology 3
PC
prevention & control
PX
psychology
RT
radiotherapy 1
RH
rehabilitation
SU
surgery
TH
therapy 10
UR
urine
VE
veterinary
VI
virology

C Diseases
C10 Nervous System Diseases 1 878
C10.668 Neuromuscular Diseases 330
C10.668.829 Peripheral Nervous System Diseases 491
C10.668.829.800 Polyneuropathies 343
C10.668.829.800.050 Alcoholic Neuropathy 18
C10.668.829.800.175 Hereditary Sensory and Autonomic Neuropathies 26
C10.668.829.800.300 Hereditary Sensory and Motor Neuropathy 71
C10.668.829.800.662 Paraneoplastic Polyneuropathy 14
C10.668.829.800.700 POEMS Syndrome 35
C10.668.829.800.750 Polyradiculoneuropathy 68
C10.668.829.800.875 Tangier Disease 3
C15 Hemic and Lymphatic Diseases 91
C15.378 Hematologic Diseases 975
C15.378.147 Blood Protein Disorders 126
C15.378.147.780 Paraproteinemias 289
C15.378.147.780.243 Cryoglobulinemia 72
C15.378.147.780.490 Heavy Chain Disease 8
C15.378.147.780.570 Monoclonal Gammopathy of Undetermined Significance 213
C15.378.147.780.650 Multiple Myeloma 1 782
C15.378.147.780.750 POEMS Syndrome 35
C15.378.147.780.838 Smoldering Multiple Myeloma 12
C15.378.147.780.925 Waldenstrom Macroglobulinemia 112
C16 Congenital, Hereditary, and Neonatal Diseases and Abnormalities 439
C16.131 Congenital Abnormalities 1 741
C16.131.077 Abnormalities, Multiple 330
C16.131.077.019 22q11 Deletion Syndrome 2
C16.131.077.065 Alagille Syndrome 19
C16.131.077.095 Angelman Syndrome 35
C16.131.077.121 Barth Syndrome 6
C16.131.077.130 Basal Cell Nevus Syndrome 33
C16.131.077.133 Beckwith-Wiedemann Syndrome 17
C16.131.077.137 Bloom Syndrome 11
C16.131.077.208 Branchio-Oto-Renal Syndrome 5
C16.131.077.229 Carney Complex 8
C16.131.077.245 Ciliopathies 9
C16.131.077.250 Cockayne Syndrome 4
C16.131.077.256 Costello Syndrome 3
C16.131.077.262 Cri-du-Chat Syndrome 11
C16.131.077.272 De Lange Syndrome 4
C16.131.077.299 Deaf-Blind Disorders 65
C16.131.077.313 Donohue Syndrome 1
C16.131.077.327 Down Syndrome 510
C16.131.077.350 Ectodermal Dysplasia 33
C16.131.077.371 Fraser Syndrome 2
C16.131.077.393 Gardner Syndrome 20
C16.131.077.401 Heterotaxy Syndrome 7
C16.131.077.410 Holoprosencephaly 8
C16.131.077.445 Incontinentia Pigmenti 19
C16.131.077.477 Isolated Noncompaction of the Ventricular Myocardium 11
C16.131.077.509 Laurence-Moon Syndrome 6
C16.131.077.525 LEOPARD Syndrome 11
C16.131.077.537 Loeys-Dietz Syndrome 7
C16.131.077.550 Marfan Syndrome 105
C16.131.077.578 Mobius Syndrome 10
C16.131.077.592 Monilethrix 1
C16.131.077.606 Nail-Patella Syndrome 8
C16.131.077.619 Netherton Syndrome 2
C16.131.077.633 Nevus, Sebaceous of Jadassohn 7
C16.131.077.662 Oculocerebrorenal Syndrome 9
C16.131.077.676 Orofaciodigital Syndromes 7
C16.131.077.690 Pallister-Hall Syndrome
C16.131.077.696 Pentalogy of Cantrell 1
C16.131.077.703 POEMS Syndrome 35
C16.131.077.717 Polycystic Kidney Diseases 82
C16.131.077.730 Prader-Willi Syndrome 92
C16.131.077.735 Prolidase Deficiency
C16.131.077.740 Proteus Syndrome 8
C16.131.077.745 Prune Belly Syndrome 3
C16.131.077.790 Rubella Syndrome, Congenital 20
C16.131.077.804 Rubinstein-Taybi Syndrome 12
C16.131.077.850 Short Rib-Polydactyly Syndrome 3
C16.131.077.855 Silver-Russell Syndrome 3
C16.131.077.860 Smith-Lemli-Opitz Syndrome 30
C16.131.077.879 Smith-Magenis Syndrome 2
C16.131.077.889 Sotos Syndrome 4
C16.131.077.899 Trichothiodystrophy Syndromes 1
C16.131.077.919 Trisomy 13 Syndrome 6
C16.131.077.929 Trisomy 18 Syndrome 5
C16.131.077.938 Waardenburg Syndrome 10
C16.131.077.941 Weill-Marchesani Syndrome 1
C16.131.077.944 Wolf-Hirschhorn Syndrome
C16.131.077.970 Zellweger Syndrome 10
C20 Immune System Diseases 746
C20.683 Immunoproliferative Disorders 19
C20.683.780 Paraproteinemias 289
C20.683.780.250 Cryoglobulinemia 72
C20.683.780.490 Heavy Chain Disease 8
C20.683.780.565 Immunoglobulin Light-chain Amyloidosis 37
C20.683.780.640 Monoclonal Gammopathy of Undetermined Significance 213
C20.683.780.650 Multiple Myeloma 1 782
C20.683.780.750 POEMS Syndrome 35
C20.683.780.838 Smoldering Multiple Myeloma 12
C20.683.780.925 Waldenstrom Macroglobulinemia 112

Add