Rubinsteinův-Taybiho syndrom [Rubinstein-Taybi Syndrome]

tematický
12
Termíny

otopalatodigitální syndrom
Rubinstein-Taybi syndrom
Rubinsteinův-Taybiův syndrom
syndrom širokých palců

 

Broad Thumb-Hallux Syndrome
Broad Thumbs and Great Toes, Characteristic Facies, and Mental Retardation
Rubinstein Syndrome

Perzistentní odkaz   https://www.medvik.cz/link/D012415
Definice

Vrozená anomálie s mentální retardací, velkými palci na rukou i nohou, antimongoloidním sklonem očí, tenkým zobákovitým nosem, nízko posazenýma ušima, srdečními anomáliemi a často malým vzrůstem. Způsoben mikrodelecí 16p13, někdy též nazýván otopalatodigitální syndrom. (cit. Velký lékařský slovník online, 2013 http://lekarske.slovniky.cz/ )

A chromosomal disorder characterized by MENTAL RETARDATION, broad thumbs, webbing of fingers and toes, beaked nose, short upper lip, pouting lower lip, agenesis of corpus callosum, large foramen magnum, keloid formation, pulmonary stenosis, vertebral anomalies, chest wall anomalies, sleep apnea, and megacolon. The disease has an autosomal dominant pattern of inheritance and is associated with deletions of the short arm of chromosome 16 (16p13.3).

DUI
D012415 MeSH Prohlížeč
CUI
M0019298
Předchozí užití
Abnormalities, Multiple (1968-1971); Mental Retardation (1966-1971)
Historická pozn.
91(72); was see under ABNORMALITIES, MULTIPLE 1972-90
Veřejná pozn.
91; was see under ABNORMALITIES, MULTIPLE 1972-90

C Nemoci
C05.116 nemoci kostí 792
C05.116.099.370 dysostóza 22
C05.116.099.370.231 kraniofaciální dysostóza 28
C05.116.099.370.380 fokální dermální hypoplazie 6
C05.116.099.370.535 Klippelův-Feilův syndrom 6
C05.116.099.370.652 orofaciodigitální syndromy 7
C05.116.099.370.797 Rubinsteinův-Taybiho syndrom 12
C05.116.099.370.894 synostóza 29
C05.660.207.103 syndrom delece 22q11 2
C05.660.207.219 Costellův syndrom 3
C05.660.207.240 kraniosynostózy 55
C05.660.207.325 Donohueův syndrom 1
C05.660.207.410 holoprosencefalie 8
C05.660.207.532 Loeysův-Dietzův syndrom 7
C05.660.207.536 megalencefalie 7
C05.660.207.620 mikrocefalie 78
C05.660.207.690 Noonanové syndrom 51
C05.660.207.707 plagiocefalie 3
C05.660.207.720 platybazie 12
C10.597.606.360 mentální retardace 1 027
C10.597.606.360.180 syndrom kočičího mňoukání 11
C10.597.606.360.210 de Langeové syndrom 4
C10.597.606.360.220 Downův syndrom 510
C10.597.606.360.690 Praderův-Williho syndrom 91
C10.597.606.360.700 Rubinsteinův-Taybiho syndrom 12
C10.597.606.360.835 Patauův syndrom 6
C10.597.606.360.969 syndrom WAGR 3
C10.597.606.360.970 Williamsův-Beurenův syndrom 21
C16.131 vrozené vady 1 740
C16.131.077.019 syndrom delece 22q11 2
C16.131.077.065 Alagillův syndrom 19
C16.131.077.095 Angelmanův syndrom 35
C16.131.077.121 Barthův syndrom 6
C16.131.077.137 Bloomův syndrom 11
C16.131.077.229 Carneyův komplex 8
C16.131.077.245 ciliopatie 9
C16.131.077.250 Cockayneův syndrom 4
C16.131.077.256 Costellův syndrom 3
C16.131.077.272 de Langeové syndrom 4
C16.131.077.299 hluchoslepota 65
C16.131.077.313 Donohueův syndrom 1
C16.131.077.327 Downův syndrom 510
C16.131.077.350 ektodermální dysplazie 33
C16.131.077.371 Fraserův syndrom 2
C16.131.077.393 Gardnerův syndrom 20
C16.131.077.401 heterotaxe 7
C16.131.077.410 holoprosencefalie 8
C16.131.077.445 incontinentia pigmenti 19
C16.131.077.537 Loeysův-Dietzův syndrom 7
C16.131.077.550 Marfanův syndrom 105
C16.131.077.578 Moebiův syndrom 10
C16.131.077.592 moniletrichosis 1
C16.131.077.619 Nethertonův syndrom 2
C16.131.077.696 Cantrellova pentalogie 1
C16.131.077.703 POEMS syndrom 34
C16.131.077.730 Praderův-Williho syndrom 91
C16.131.077.735 nedostatek prolidázy
C16.131.077.740 Proteův syndrom 8
C16.131.077.745 prune belly syndrom 3
C16.131.077.790 zarděnky vrozené 20
C16.131.077.889 Sotosův syndrom 4
C16.131.077.919 Patauův syndrom 6
C16.131.077.929 syndrom trizomie 18 5
C16.131.077.938 Waardenburgův syndrom 10
C16.131.077.970 Zellwegerův syndrom 10
C16.131.260.019 syndrom delece 22q11 2
C16.131.260.040 Angelmanův syndrom 35
C16.131.260.210 de Langeové syndrom 4
C16.131.260.260 Downův syndrom 510
C16.131.260.380 holoprosencefalie 8
C16.131.260.440 Jacobsenův syndrom 1
C16.131.260.700 Praderův-Williho syndrom 91
C16.131.260.905 Sotosův syndrom 4
C16.131.260.923 Patauův syndrom 6
C16.131.260.932 syndrom trizomie 18 5
C16.131.260.940 syndrom WAGR 3
C16.131.621.207.103 syndrom delece 22q11 2
C16.131.621.207.207 kleidokraniální dysplazie 7
C16.131.621.207.231 kraniofaciální dysostóza 28
C16.131.621.207.240 kraniosynostózy 55
C16.131.621.207.410 holoprosencefalie 8
C16.131.621.207.532 megalencefalie 7
C16.131.621.207.540 maxilofaciální abnormality 28
C16.131.621.207.620 mikrocefalie 78
C16.131.621.207.690 Noonanové syndrom 51
C16.131.621.207.700 orofaciodigitální syndromy 7
C16.131.621.207.707 plagiocefalie 3
C16.131.621.207.720 platybazie 12
C16.131.621.207.850 Rubinsteinův-Taybiho syndrom 12
C16.320.180.019 syndrom delece 22q11 2
C16.320.180.040 Angelmanův syndrom 35
C16.320.180.210 de Langeové syndrom 4
C16.320.180.260 Downův syndrom 510
C16.320.180.380 holoprosencefalie 8
C16.320.180.440 Jacobsenův syndrom 1
C16.320.180.700 Praderův-Williho syndrom 91
C16.320.180.905 Sotosův syndrom 4
C16.320.180.923 Patauův syndrom 6
C16.320.180.932 syndrom trizomie 18 5
C16.320.180.940 syndrom WAGR 3