Prune Belly Syndrome [prune belly syndrom]

topical
3
Terms

Eagleův-Barrettův syndrom
syndrom svraštělého bříška

 

Abdominal Muscle Deficiency Syndrome
Congenital Absence of the Abdominal Muscles
Eagle-Barrett Syndrome
Obrinsky Syndrome
Prune-Belly Syndrome

Persistent link   https://www.medvik.cz/link/D011535
Definition

A syndrome characterized by abdominal wall musculature deficiency, cryptorchism, and urinary tract abnormalities. The syndrome derives its name from its characteristic distended abdomen with wrinkled skin.

Annotation
a syndrome of multiple abnorm; do not use /congen & do not coord with INFANT, NEWBORN, DISEASES
DUI
D011535 MeSH Browser
CUI
M0017933
Previous indexing
Abnormalities, Multiple (1968-1981); Abdominal Wall/AB (1966-1981); Cryptorchism (1966-1981); Urogenital System/AB (1966-1981)
History note
82
Public note
82

C Diseases
C01 Infections 2 026
C04 Neoplasms 12 774
C11 Eye Diseases 1 489
C16.131.077.019 22q11 Deletion Syndrome 2
C16.131.077.065 Alagille Syndrome 19
C16.131.077.095 Angelman Syndrome 35
C16.131.077.121 Barth Syndrome 6
C16.131.077.130 Basal Cell Nevus Syndrome 33
C16.131.077.137 Bloom Syndrome 11
C16.131.077.229 Carney Complex 8
C16.131.077.245 Ciliopathies 9
C16.131.077.250 Cockayne Syndrome 4
C16.131.077.256 Costello Syndrome 3
C16.131.077.262 Cri-du-Chat Syndrome 11
C16.131.077.272 De Lange Syndrome 4
C16.131.077.299 Deaf-Blind Disorders 65
C16.131.077.313 Donohue Syndrome 1
C16.131.077.327 Down Syndrome 510
C16.131.077.350 Ectodermal Dysplasia 33
C16.131.077.371 Fraser Syndrome 2
C16.131.077.393 Gardner Syndrome 20
C16.131.077.401 Heterotaxy Syndrome 7
C16.131.077.410 Holoprosencephaly 8
C16.131.077.445 Incontinentia Pigmenti 19
C16.131.077.509 Laurence-Moon Syndrome 6
C16.131.077.525 LEOPARD Syndrome 11
C16.131.077.537 Loeys-Dietz Syndrome 7
C16.131.077.550 Marfan Syndrome 105
C16.131.077.578 Mobius Syndrome 10
C16.131.077.592 Monilethrix 1
C16.131.077.606 Nail-Patella Syndrome 8
C16.131.077.619 Netherton Syndrome 2
C16.131.077.676 Orofaciodigital Syndromes 7
C16.131.077.696 Pentalogy of Cantrell 1
C16.131.077.703 POEMS Syndrome 35
C16.131.077.717 Polycystic Kidney Diseases 82
C16.131.077.730 Prader-Willi Syndrome 92
C16.131.077.735 Prolidase Deficiency
C16.131.077.740 Proteus Syndrome 8
C16.131.077.745 Prune Belly Syndrome 3
C16.131.077.804 Rubinstein-Taybi Syndrome 12
C16.131.077.855 Silver-Russell Syndrome 3
C16.131.077.860 Smith-Lemli-Opitz Syndrome 30
C16.131.077.879 Smith-Magenis Syndrome 2
C16.131.077.889 Sotos Syndrome 4
C16.131.077.919 Trisomy 13 Syndrome 6
C16.131.077.929 Trisomy 18 Syndrome 5
C16.131.077.938 Waardenburg Syndrome 10
C16.131.077.941 Weill-Marchesani Syndrome 1
C16.131.077.970 Zellweger Syndrome 10

Diastasis Recti And Weakness Of The Linea Alba Disease MeSH Browser

Prune Belly Syndrome with Pulmonic Stenosis, Mental Retardation, and Deafness Disease MeSH Browser

Urethral obstruction sequence Disease MeSH Browser