Incontinentia Pigmenti [incontinentia pigmenti]
- Terms
-
Blochův-Sulzbergerův syndrom
melanoblastosis Bloch-Sulzberg
melanoblastosis cutis linearis sive systematica
naevus pigmentosus systematicus
Siemensův-Blochův-Sulzbergův syndrom
-
Bloch-Siemens Syndrome
Bloch-Siemens-Sulzberger Syndrome
Bloch-Sulzberger Syndrome
A genodermatosis occurring mostly in females and characterized by skin changes in three phases - vesiculobullous, verrucous papillomatous, and macular melanodermic. Hyperpigmentation is bizarre and irregular. Sixty percent of patients have abnormalities of eyes, teeth, central nervous system, and skin appendages.
- Annotation
- multiple skin & other abnorm; do not confuse with INCONTINENTIA PIGMENTI ACHROMIANS see PIGMENTATION DISORDERS
- DUI
- D007184 MeSH Browser
- CUI
- M0011200
- Previous indexing
- Pigmentation Disorders (1966-1986)
- History note
- 91(87); was see under PIGMENTATION DISORDERS 1987-90
- Public note
- 91; was see under PIGMENTATION DISORDERS 1987-90
Allowable subheadings
- BL
- blood
- CF
- cerebrospinal fluid
- CI
- chemically induced
- CL
- classification 1
- CO
- complications 1
- DI
- diagnosis 13
- DG
- diagnostic imaging
- DH
- diet therapy
- DT
- drug therapy
- EC
- economics
- EM
- embryology
- EN
- enzymology
- EP
- epidemiology
- EH
- ethnology
- ET
- etiology 4
- GE
- genetics 7
- HI
- history
- IM
- immunology
- ME
- metabolism
- MI
- microbiology
- MO
- mortality
- NU
- nursing
- PS
- parasitology
- PA
- pathology 2
- PP
- physiopathology
- PC
- prevention & control
- PX
- psychology
- RT
- radiotherapy
- RH
- rehabilitation
- SU
- surgery
- TH
- therapy 4
- UR
- urine
- VE
- veterinary
- VI
- virology
Incontinentia pigmenti, familial male-lethal type Disease MeSH Browser