Familial Hypophosphatemic Rickets [familiární hypofosfatemická rachitida]

topical
28
Terms

dědičná hypofosfatemická rachitida
dědičná vitamin D rezistentní rachitida
hypofosfatemická rachitida dominantní vázaná na chromozóm X
hypofosfatemická rachitida recesivní vázaná na chromozóm X
hypofosfatemická rachitida vázaná na chromozóm X
hypofosfatemická vitamin D rezistentní rachitida
hypofosfatémie vázaná na chromozóm X
primární vitamin D rezistentní křivice
vitamin D-rezistentní rachitida vázaná na chromozóm X
vitamin D-rezistentní rachitis
X-vázaná dominantní hypofosfatemická rachitida
X-vázaná hypofosfatemická křivice
X-vázaná hypofosfatemická rachitida
X-vázaná recesivní hypofosfatemická rachitida
X-vázaná recesivní hypofosfatemická rachitis
X-vázaná vitamin D-rezistentní rachitida

 

Generalized Resistance To 1,25-Dihydroxyvitamin D
Hereditary Hypophosphatemic Rickets
Hereditary Vitamin D-Resistant Rickets
Hypocalcemic Vitamin D-Resistant Rickets
Hypophosphatemia, X-Linked
Hypophosphatemic Rickets, X-Linked Dominant
Hypophosphatemic Rickets, X-Linked Recessive
Rickets, Hereditary Vitamin D-Resistant
Rickets, X-Linked Hypophosphatemic
Vitamin D-Resistant Rickets With End-Organ Unresponsiveness To 1,25-Dihydroxycholecalciferol
Vitamin D-Resistant Rickets, Hereditary
Vitamin D-Resistant Rickets, X-Linked
X-Linked Hypophosphatemia

Persistent link   https://www.medvik.cz/link/D053098
Definition

A hereditary disorder characterized by HYPOPHOSPHATEMIA; RICKETS; OSTEOMALACIA; renal defects in phosphate reabsorption and vitamin D metabolism; and growth retardation. Autosomal and X-linked dominant and recessive variants have been reported.

Annotation
coordinate with GENETIC DISEASES, X-LINKED if X-linked variant is discussed
DUI
D053098 MeSH Browser
CUI
M0577083
Previous indexing
Hypophosphatemia, Familial (1965-2006); Rickets (1965-2006); Vitamin D (1965-2006)
History note
2014 (2007); use HYPOPHOSPHATEMIA, FAMILIAL 1994-2006, use RICKETS, VITAMIN D-RESISTANT 1972-1993
Public note
2014; see HYPOPHOSPHATEMIC RICKETS, X-LINKED DOMINANT 2006-2013; see HYPOPHOSPHATEMIA, FAMILIAL 1994-2006, see RICKETS, VITAMIN D-RESISTANT 1972-1993

C Diseases
C05.116 Bone Diseases 796
C05.116.198.816 Rickets 143
C05.116.198.816.875 Rickets, Hypophosphatemic 6
C05.116.198.816.875.500 Familial Hypophosphatemic Rickets 28
C12.050.351.968 Urologic Diseases 836
C12.050.351.968.419 Kidney Diseases 3 067
C12.050.351.968.419.815 Renal Tubular Transport, Inborn Errors 36
C12.050.351.968.419.815.647 Hypophosphatemia, Familial 12
C12.050.351.968.419.815.647.500 Familial Hypophosphatemic Rickets 28
C12.200.777 Urologic Diseases 836
C12.200.777.419 Kidney Diseases 3 067
C12.200.777.419.815.647 Hypophosphatemia, Familial 12
C12.200.777.419.815.647.500 Familial Hypophosphatemic Rickets 28
C12.950.419 Kidney Diseases 3 067
C12.950.419.815.647 Hypophosphatemia, Familial 12
C12.950.419.815.647.500 Familial Hypophosphatemic Rickets 28
C16.320.565.618.544 Hypophosphatemia, Familial 12
C16.320.565.618.544.500 Familial Hypophosphatemic Rickets 28
C16.320.831.647 Hypophosphatemia, Familial 12
C18.452 Metabolic Diseases 1 200
C18.452.104.816 Rickets 143
C18.452.104.816.875 Rickets, Hypophosphatemic 6
C18.452.104.816.875.500 Familial Hypophosphatemic Rickets 28
C18.452.174.845 Rickets 143
C18.452.174.845.875 Rickets, Hypophosphatemic 6
C18.452.174.845.875.500 Familial Hypophosphatemic Rickets 28
C18.452.648.618.544 Hypophosphatemia, Familial 12
C18.452.648.618.544.500 Familial Hypophosphatemic Rickets 28
C18.452.750.400 Hypophosphatemia 51
C18.452.750.400.500 Hypophosphatemia, Familial 12
C18.452.750.400.500.500 Familial Hypophosphatemic Rickets 28
C18.452.750.400.750 Rickets, Hypophosphatemic 6
C18.452.750.400.750.500 Familial Hypophosphatemic Rickets 28
C18.654 Nutrition Disorders 1 032
C18.654.521 Malnutrition 643
C18.654.521.500 Deficiency Diseases 71
C18.654.521.500.133 Avitaminosis 101
C18.654.521.500.133.770 Vitamin D Deficiency 578
C18.654.521.500.133.770.734 Rickets 143
C18.654.521.500.133.770.734.875 Rickets, Hypophosphatemic 6
C18.654.521.500.133.770.734.875.500 Familial Hypophosphatemic Rickets 28

Hypophosphatemic Rickets with Hypercalciuria, Hereditary Disease MeSH Browser

Hypophosphatemic Rickets, Autosomal Dominant Disease MeSH Browser

Hypophosphatemic Rickets, Autosomal Recessive, 1 Disease MeSH Browser

Hypophosphatemic Rickets, Autosomal Recessive, 2 Disease MeSH Browser

Vitamin D Hydroxylation-Deficient Rickets, Type 1A Disease MeSH Browser

Vitamin D Hydroxylation-Deficient Rickets, Type 1B Disease MeSH Browser

Vitamin D-Dependent Rickets, Type 2A Disease MeSH Browser

Vitamin D-Dependent Rickets, Type 2B, With Normal Vitamin D Receptor Disease MeSH Browser